徳島大学病院における先天性血友病患者（成人例）の実態調査 : 移行期医療の重要性

機関リポジトリ Web Site

書誌事項

タイトル別名
  • トクシマ ダイガク ビョウイン ニ オケル センテンセイ ケツユウビョウ カンジャ(セイジンレイ)ノ ジッタイ チョウサ : イコウキ イリョウ ノ ジュウヨウセイ : ダイ26カイ ワカテ ショウレイショウ ジュショウ ロンブン
  • Transitional Care of Adult Congenital Hemophilia Patients in Tokushima University Hospital
  • 先天性血友病患者の移行期の実態

この論文をさがす

抄録

【Introduction】Congenital hemophilia is a category of hemorrhagic disease caused by a genetic defect in the production of coagulation factors. It is treated by administering regular coagulation factor injections on an ongoing basis. Hemophilia is a hereditary illness, often causing social and psychological problems as a result of the disease. To analyze the objective effects of hemophilia, we conducted a retrospective analysis in Tokushima University Hospital. 【Result】All ２３ cases were men between the ages of２０and７２. Hemophilia A was present in１７cases, and hemophilia B was present in six. Nineteen out of ２３ cases were severe, and the others were intermediate. Medical assessments were conducted at pediatrics in seven cases and hematology in １６ cases. Adoption of the self-injection technique was not realized in five cases. Seventeen cases were complicated by hemophilic arthropathy, seven with human immunodeficiency virus（HIV）, and １２ with hepatitis C virus. Eight participants were unemployed, and１７were unmarried. 【Discussion】 Many adult hemophilia patients still visit pediatrics in our hospital. Hemophilia in the period of growth between adolescence and young adulthood is often accompanied by life-altering events such as entering higher education, marriage, and work experience. Therefore, collaboration among professionals of multiple occupations, such as doctors, nurses, pharmacists, medical social workers, and clinical psychologists, is essential. Furthermore, there are many cases of HIV and hepatitis C virus infections complicating hemophilia study due to the stigma surrounding HIV-tainted blood. 【Conclusion】It is imperative that we establish a long-term, sustainable, and multi-disciplinary transitional care and medical support system for patients and their families.

収録刊行物

キーワード

詳細情報 詳細情報について

問題の指摘

ページトップへ