{"@context":{"@vocab":"https://cir.nii.ac.jp/schema/1.0/","rdfs":"http://www.w3.org/2000/01/rdf-schema#","dc":"http://purl.org/dc/elements/1.1/","dcterms":"http://purl.org/dc/terms/","foaf":"http://xmlns.com/foaf/0.1/","prism":"http://prismstandard.org/namespaces/basic/2.0/","cinii":"http://ci.nii.ac.jp/ns/1.0/","datacite":"https://schema.datacite.org/meta/kernel-4/","ndl":"http://ndl.go.jp/dcndl/terms/","jpcoar":"https://github.com/JPCOAR/schema/blob/master/2.0/"},"@id":"https://cir.nii.ac.jp/crid/1360565166754229632.json","@type":"Article","productIdentifier":[{"identifier":{"@type":"DOI","@value":"10.1038/ncb1812"}},{"identifier":{"@type":"URI","@value":"http://www.nature.com/articles/ncb1812.pdf"}},{"identifier":{"@type":"URI","@value":"http://www.nature.com/articles/ncb1812"}},{"identifier":{"@type":"DOI","@value":"10.1016/j.bpj.2008.12.1824"}},{"identifier":{"@type":"PMID","@value":"19122591"}}],"resourceType":"学術雑誌論文(journal article)","dc:title":[{"@value":"MG53 nucleates assembly of cell membrane repair machinery"}],"description":[{"notation":[{"@value":"Dynamic membrane repair and remodelling is an elemental process that maintains cell integrity and mediates efficient cellular function. Here we report that MG53, a muscle-specific tripartite motif family protein (TRIM72), is a component of the sarcolemmal membrane-repair machinery. MG53 interacts with phosphatidylserine to associate with intracellular vesicles that traffic to and fuse with sarcolemmal membranes. Mice null for MG53 show progressive myopathy and reduced exercise capability, associated with defective membrane-repair capacity. Injury of the sarcolemmal membrane leads to entry of the extracellular oxidative environment and MG53 oligomerization, resulting in recruitment of MG53-containing vesicles to the injury site. After vesicle translocation, entry of extracellular Ca(2+) facilitates vesicle fusion to reseal the membrane. Our data indicate that intracellular vesicle translocation and Ca(2+)-dependent membrane fusion are distinct steps involved in the repair of membrane damage and that MG53 may initiate the assembly of the membrane repair machinery in an oxidation-dependent manner."}]}],"creator":[{"@id":"https://cir.nii.ac.jp/crid/1380284919966607493","@type":"Researcher","foaf:name":[{"@value":"Chuanxi Cai"}]},{"@id":"https://cir.nii.ac.jp/crid/1380284919966607489","@type":"Researcher","foaf:name":[{"@value":"Haruko Masumiya"}]},{"@id":"https://cir.nii.ac.jp/crid/1380284919966607498","@type":"Researcher","foaf:name":[{"@value":"Noah Weisleder"}]},{"@id":"https://cir.nii.ac.jp/crid/1380284919966607617","@type":"Researcher","foaf:name":[{"@value":"Noriyuki Matsuda"}]},{"@id":"https://cir.nii.ac.jp/crid/1420845751152529408","@type":"Researcher","personIdentifier":[{"@type":"KAKEN_RESEARCHERS","@value":"60183894"},{"@type":"NRID","@value":"1000060183894"},{"@type":"NRID","@value":"9000001692913"},{"@type":"NRID","@value":"9000391612814"},{"@type":"NRID","@value":"9000005394242"},{"@type":"NRID","@value":"9000241640261"},{"@type":"NRID","@value":"9000018130323"},{"@type":"NRID","@value":"9000003781474"},{"@type":"NRID","@value":"9000022487120"},{"@type":"NRID","@value":"9000241640202"},{"@type":"NRID","@value":"9000006924239"},{"@type":"NRID","@value":"9000240176063"},{"@type":"RESEARCHMAP","@value":"https://researchmap.jp/7000009454"}],"foaf:name":[{"@value":"Miyuki Nishi"}]},{"@id":"https://cir.nii.ac.jp/crid/1380284919966607491","@type":"Researcher","foaf:name":[{"@value":"Moonsun Hwang"}]},{"@id":"https://cir.nii.ac.jp/crid/1380284919966607494","@type":"Researcher","foaf:name":[{"@value":"Jae-Kyun Ko"}]},{"@id":"https://cir.nii.ac.jp/crid/1380284919966607616","@type":"Researcher","foaf:name":[{"@value":"Peihui Lin"}]},{"@id":"https://cir.nii.ac.jp/crid/1380284919966607496","@type":"Researcher","foaf:name":[{"@value":"Angela Thornton"}]},{"@id":"https://cir.nii.ac.jp/crid/1380284919966607490","@type":"Researcher","foaf:name":[{"@value":"Xiaoli Zhao"}]},{"@id":"https://cir.nii.ac.jp/crid/1380284919966607619","@type":"Researcher","foaf:name":[{"@value":"Zui Pan"}]},{"@id":"https://cir.nii.ac.jp/crid/1380284919966607492","@type":"Researcher","foaf:name":[{"@value":"Shinji Komazaki"}]},{"@id":"https://cir.nii.ac.jp/crid/1380284919966607618","@type":"Researcher","foaf:name":[{"@value":"Marco Brotto"}]},{"@id":"https://cir.nii.ac.jp/crid/1380284919966607495","@type":"Researcher","foaf:name":[{"@value":"Hiroshi Takeshima"}]},{"@id":"https://cir.nii.ac.jp/crid/1380284919966607497","@type":"Researcher","foaf:name":[{"@value":"Jianjie Ma"}]}],"publication":{"publicationIdentifier":[{"@type":"PISSN","@value":"14657392"},{"@type":"EISSN","@value":"14764679"},{"@type":"PISSN","@value":"00063495"}],"prism:publicationName":[{"@value":"Nature Cell Biology"}],"dc:publisher":[{"@value":"Springer Science and Business Media LLC"}],"prism:publicationDate":"2008-11-30","prism:volume":"11","prism:number":"1","prism:startingPage":"56","prism:endingPage":"64"},"reviewed":"false","dcterms:accessRights":"http://purl.org/coar/access_right/c_abf2","dc:rights":["http://www.springer.com/tdm"],"url":[{"@id":"http://www.nature.com/articles/ncb1812.pdf"},{"@id":"http://www.nature.com/articles/ncb1812"}],"createdAt":"2008-11-30","modifiedAt":"2023-05-21","foaf:topic":[{"@id":"https://cir.nii.ac.jp/all?q=Male","dc:title":"Male"},{"@id":"https://cir.nii.ac.jp/all?q=Mice,%20Knockout","dc:title":"Mice, Knockout"},{"@id":"https://cir.nii.ac.jp/all?q=Muscle%20Fibers,%20Skeletal","dc:title":"Muscle Fibers, Skeletal"},{"@id":"https://cir.nii.ac.jp/all?q=Biophysics","dc:title":"Biophysics"},{"@id":"https://cir.nii.ac.jp/all?q=Membrane%20Proteins","dc:title":"Membrane Proteins"},{"@id":"https://cir.nii.ac.jp/all?q=Muscle%20Proteins","dc:title":"Muscle Proteins"},{"@id":"https://cir.nii.ac.jp/all?q=Extracellular%20Fluid","dc:title":"Extracellular Fluid"},{"@id":"https://cir.nii.ac.jp/all?q=Membrane%20Fusion","dc:title":"Membrane Fusion"},{"@id":"https://cir.nii.ac.jp/all?q=Cell%20Line","dc:title":"Cell Line"},{"@id":"https://cir.nii.ac.jp/all?q=Mice","dc:title":"Mice"},{"@id":"https://cir.nii.ac.jp/all?q=Oxidative%20Stress","dc:title":"Oxidative Stress"},{"@id":"https://cir.nii.ac.jp/all?q=Protein%20Transport","dc:title":"Protein Transport"},{"@id":"https://cir.nii.ac.jp/all?q=Sarcolemma","dc:title":"Sarcolemma"},{"@id":"https://cir.nii.ac.jp/all?q=Animals,%20Newborn","dc:title":"Animals, Newborn"},{"@id":"https://cir.nii.ac.jp/all?q=Animals","dc:title":"Animals"},{"@id":"https://cir.nii.ac.jp/all?q=Regeneration","dc:title":"Regeneration"},{"@id":"https://cir.nii.ac.jp/all?q=Calcium%20Signaling","dc:title":"Calcium Signaling"},{"@id":"https://cir.nii.ac.jp/all?q=Carrier%20Proteins","dc:title":"Carrier Proteins"},{"@id":"https://cir.nii.ac.jp/all?q=Transport%20Vesicles","dc:title":"Transport Vesicles"},{"@id":"https://cir.nii.ac.jp/all?q=Cells,%20Cultured","dc:title":"Cells, Cultured"}],"project":[{"@id":"https://cir.nii.ac.jp/crid/1040282257052279296","@type":"Project","projectIdentifier":[{"@type":"KAKEN","@value":"21500382"},{"@type":"JGN","@value":"JP21500382"},{"@type":"URI","@value":"https://kaken.nii.ac.jp/grant/KAKENHI-PROJECT-21500382/"}],"notation":[{"@language":"ja","@value":"小胞体タンパク質ミツグミン23の機能解析"},{"@language":"en","@value":"Functional analysis of SR protein, Mitsugumin 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sarcolemma"}]},{"@id":"https://cir.nii.ac.jp/crid/1363670319921500928","@type":"Article","relationType":["references"],"jpcoar:relatedTitle":[{"@value":"Cell Membrane Resealing by a Vesicular Mechanism Similar to Neurotransmitter Release"}]},{"@id":"https://cir.nii.ac.jp/crid/1363670320082376064","@type":"Article","relationType":["references"],"jpcoar:relatedTitle":[{"@value":"Ca2+-bridging mechanism and phospholipid head group recognition in the membrane-binding protein annexin V"}]},{"@id":"https://cir.nii.ac.jp/crid/1363670320128619520","@type":"Article","relationType":["references"],"jpcoar:relatedTitle":[{"@value":"Excitation-contraction uncoupling and muscular degeneration in mice lacking functional skeletal muscle ryanodine-receptor gene"}]},{"@id":"https://cir.nii.ac.jp/crid/1363951793286181376","@type":"Article","relationType":["references"],"jpcoar:relatedTitle":[{"@value":"Defective membrane repair in dysferlin-deficient muscular 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