{"@context":{"@vocab":"https://cir.nii.ac.jp/schema/1.0/","rdfs":"http://www.w3.org/2000/01/rdf-schema#","dc":"http://purl.org/dc/elements/1.1/","dcterms":"http://purl.org/dc/terms/","foaf":"http://xmlns.com/foaf/0.1/","prism":"http://prismstandard.org/namespaces/basic/2.0/","cinii":"http://ci.nii.ac.jp/ns/1.0/","datacite":"https://schema.datacite.org/meta/kernel-4/","ndl":"http://ndl.go.jp/dcndl/terms/","jpcoar":"https://github.com/JPCOAR/schema/blob/master/2.0/"},"@id":"https://cir.nii.ac.jp/crid/1361137045016534656.json","@type":"Article","productIdentifier":[{"identifier":{"@type":"DOI","@value":"10.1038/nrgastro.2010.81"}},{"identifier":{"@type":"URI","@value":"http://www.nature.com/articles/nrgastro.2010.81.pdf"}},{"identifier":{"@type":"URI","@value":"http://www.nature.com/articles/nrgastro.2010.81"}},{"identifier":{"@type":"PMID","@value":"20548323"}}],"dc:title":[{"@value":"Autoimmune pancreatitis and IgG4-related sclerosing disease"}],"description":[{"notation":[{"@value":"Autoimmune pancreatitis (AIP) is a unique form of pancreatitis in which the pathogenesis is suspected to involve autoimmune mechanisms. AIP sometimes mimics pancreatic cancer in its presentation, but as AIP responds dramatically to steroid therapy, accurate diagnosis is necessary. AIP is currently diagnosed on the basis of a combination of characteristic clinical, serological, morphological and histopathological features. However, its diagnosis remains a clinical challenge and there are no internationally agreed diagnostic criteria. Another type of AIP called 'idiopathic duct-centric chronic pancreatitis' or 'AIP with granulocytic epithelial lesion' has been reported in Western countries. IgG4-related sclerosing disease is a systemic disease in which IgG4-positive plasma cells and T lymphocytes extensively infiltrate various organs. Organs with tissue fibrosis and obliterative phlebitis, such as the pancreas, salivary gland and retroperitoneum, show clinical manifestations; AIP seems to represent one manifestation of IgG4-related sclerosing disease. As a mass is formed in most cases of IgG4-related sclerosing disease, a malignant tumor is frequently suspected on initial presentation. Clinicians should consider IgG4-related sclerosing disease in the differential diagnosis to avoid unnecessary surgery."}]}],"creator":[{"@id":"https://cir.nii.ac.jp/crid/1381137045016534532","@type":"Researcher","foaf:name":[{"@value":"Terumi Kamisawa"}]},{"@id":"https://cir.nii.ac.jp/crid/1381137045016534530","@type":"Researcher","foaf:name":[{"@value":"Kensuke Takuma"}]},{"@id":"https://cir.nii.ac.jp/crid/1381137045016534529","@type":"Researcher","foaf:name":[{"@value":"Naoto Egawa"}]},{"@id":"https://cir.nii.ac.jp/crid/1381137045016534531","@type":"Researcher","foaf:name":[{"@value":"Koji Tsuruta"}]},{"@id":"https://cir.nii.ac.jp/crid/1381137045016534528","@type":"Researcher","foaf:name":[{"@value":"Tsuneo Sasaki"}]}],"publication":{"publicationIdentifier":[{"@type":"PISSN","@value":"17595045"},{"@type":"EISSN","@value":"17595053"}],"prism:publicationName":[{"@value":"Nature Reviews Gastroenterology & Hepatology"}],"dc:publisher":[{"@value":"Springer Science and Business Media LLC"}],"prism:publicationDate":"2010-06-15","prism:volume":"7","prism:number":"7","prism:startingPage":"401","prism:endingPage":"409"},"reviewed":"false","dc:rights":["http://www.springer.com/tdm"],"url":[{"@id":"http://www.nature.com/articles/nrgastro.2010.81.pdf"},{"@id":"http://www.nature.com/articles/nrgastro.2010.81"}],"createdAt":"2010-06-15","modifiedAt":"2023-05-19","foaf:topic":[{"@id":"https://cir.nii.ac.jp/all?q=Sclerosis","dc:title":"Sclerosis"},{"@id":"https://cir.nii.ac.jp/all?q=T-Lymphocytes","dc:title":"T-Lymphocytes"},{"@id":"https://cir.nii.ac.jp/all?q=Plasma%20Cells","dc:title":"Plasma Cells"},{"@id":"https://cir.nii.ac.jp/all?q=Autoimmune%20Diseases","dc:title":"Autoimmune Diseases"},{"@id":"https://cir.nii.ac.jp/all?q=Diagnosis,%20Differential","dc:title":"Diagnosis, Differential"},{"@id":"https://cir.nii.ac.jp/all?q=Pancreatitis","dc:title":"Pancreatitis"},{"@id":"https://cir.nii.ac.jp/all?q=Immunoglobulin%20G","dc:title":"Immunoglobulin G"},{"@id":"https://cir.nii.ac.jp/all?q=Humans","dc:title":"Humans"}],"relatedProduct":[{"@id":"https://cir.nii.ac.jp/crid/1360025431125831808","@type":"Article","resourceType":"学術雑誌論文(journal article)","relationType":["isReferencedBy"],"jpcoar:relatedTitle":[{"@value":"Aberrant Methylation of\n                    <i>RUNX1</i>\n                    is Associated with the Pathogenesis of Autoimmune Pancreatitis"}]},{"@id":"https://cir.nii.ac.jp/crid/1360283690303196288","@type":"Article","resourceType":"学術雑誌論文(journal article)","relationType":["isReferencedBy"],"jpcoar:relatedTitle":[{"@value":"The role of peroral video cholangioscopy in patients with IgG4-related sclerosing cholangitis"}]},{"@id":"https://cir.nii.ac.jp/crid/1360283690917542528","@type":"Article","resourceType":"学術雑誌論文(journal article)","relationType":["isReferencedBy"],"jpcoar:relatedTitle":[{"@value":"Diagnosis of autoimmune pancreatitis by EUS-FNA by using a 22-gauge needle based on the International Consensus 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