A Case of Atypical Absence Status Controlled by Corpus Callosotomy

Yonee Chihiro, Maruyama Shinsuke, Matsufuji Mayumi, Sano Nozomi, Sato Masanori, Hosoyama Hiroshi, Hanaya Ryosuke

doi:10.3805/jjes.40.541

<p>Corpus callosotomy is considered the most effective procedure for preventing tonic, atonic, and other seizures causing a fall. This study reports a case of a 6-year-old female, diagnosed with trisomy 21 following birth, wherein corpus callosotomy was effective for the treatment of atypical absence status epilepticus. She developed West syndrome at eight months of age. At 5 years, she experienced multiple seizure types, including tonic, myoclonic, and atypical absence seizures. She was hospitalized at 6 years 0 months, because of her inability to walk and difficulty in eating with the increase in atypical absence seizures to more than 100 times a day. The condition was intractable and corpus callosotomy was performed at 6 years and 1 month. The postoperative electroencephalogram revealed generalized spike-wave complexes localized to the right frontal area. Two years have passed since, and her seizures have disappeared. There have been several reports regarding the effects of corpus callosotomy on atypical absence seizures. This case suggests that corpus callosotomy may be a prominent treatment option for intractable atypical absence seizures.</p>

A Case of Atypical Absence Status Controlled by Corpus Callosotomy

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