繰り返す体幹失調と異常眼球運動を呈したOpsoclonus-myoclonus syndrome例

書誌事項

タイトル別名
  • A Case of Opsoclonus-myoclonus Syndrome with Repeated Truncal Ataxia and Chaotic Saccadic Eye Movement
  • 臨床 繰り返す体幹失調と異常眼球運動を呈したOpsoclonus-myoclonus syndrome例
  • リンショウ クリカエス カラダ カン シッチョウ ト イジョウ ガンキュウ ウンドウ オ テイシタ Opsoclonus-myoclonus syndromeレイ
公開日
2014
DOI
  • 10.5631/jibirin.107.603
  • 10.5631/jibirinsuppl.141.8
公開者
耳鼻咽喉科臨床学会

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説明

The opsoclonus-myoclonus syndrome (OMS) is characterized by subacute onset of opsoclonus, a disorder causing of saccadic eye movements causing involuntary, chaotic saccades that occur in all directions. <br>We report herein on a 36-year-old man with mainly horizontal chaotic saccades after truncal ataxia. Intravenous corticosteroids pulse therapy was very effective and his opsoclonus disappeared. No malignant tumors were detected with positron emission tomography. We analyzed eye movement using electronystagmography (ENG) and considered this case to be one of non-paraneoplastic OMS.

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