{"@context":{"@vocab":"https://cir.nii.ac.jp/schema/1.0/","rdfs":"http://www.w3.org/2000/01/rdf-schema#","dc":"http://purl.org/dc/elements/1.1/","dcterms":"http://purl.org/dc/terms/","foaf":"http://xmlns.com/foaf/0.1/","prism":"http://prismstandard.org/namespaces/basic/2.0/","cinii":"http://ci.nii.ac.jp/ns/1.0/","datacite":"https://schema.datacite.org/meta/kernel-4/","ndl":"http://ndl.go.jp/dcndl/terms/","jpcoar":"https://github.com/JPCOAR/schema/blob/master/2.0/"},"@id":"https://cir.nii.ac.jp/crid/1390282679819005824.json","@type":"Article","productIdentifier":[{"identifier":{"@type":"DOI","@value":"10.4295/audiology.53.142"}},{"identifier":{"@type":"NAID","@value":"130004544880"}},{"identifier":{"@type":"NAID","@value":"10026423025"}},{"identifier":{"@type":"URI","@value":"https://search.jamas.or.jp/link/ui/2010194884"}}],"dc:title":[{"@language":"en","@value":"Idiopathic bilateral sensorineural hearing loss (IBSH): Clinical study of cases with rapidly progressive and slowly progressive deafness."},{"@language":"ja","@value":"特発性両側性感音難聴の検討―進行様式の差による検討―"}],"dcterms:alternative":[{"@language":"ja","@value":"—進行様式の差による検討—"}],"dc:language":"ja","description":[{"type":"abstract","notation":[{"@language":"en","@value":"We investigated the clinical differences between a group of IBSH patients with rapidly progressive hearing loss and a group of these patients with slowly progressive hearing loss. A total of 107 patients of IBSH followed up at the hearing clinic in our department for more than 10 years were enrolled. Of the 107 patients, 51 were classified into the rapidly progressive deafness group and 56 into the slowly progressive group. In regard to the age distribution, a high incidence in the 40-49 years age group was seen in the rapidly progressive deafness group and a high incidence in the 0-9 years and over 40 years age groups was found in the slowly progressive deafness group. The number of patients with vertigo in the rapidly progressive deafness group was 27 (52%), and that in the slowly progressive deafness group was 17 (30%).<br>Next, we investigated 19 patients of the rapidly progressive deafness group who presented with recurrent episodes of vertigo. In regard to the type of audiograms at the first visit, 28 ears (74%) showed a high-tone hearing loss pattern. When the cases were classified according to the frequency area of rapid deterioration in the audiograms, deterioration in the all-frequencies (250Hz-8kHz) area was found to be the most frequent.<br>We considered that in many cases in this study, recurrent vertigo were needed to be differentiated from Meniere's disease."},{"@language":"ja","@value":"10年以上経過観察できた特難107例を抽出し, 急速型 (51例) 緩徐型 (56例) に分け検討した。発症時年齢分布は緩徐型が10歳未満と40～70歳代に多く2峰性を示し, 急速型は40歳代をピークとした1峰性を示した。初診時聴力型は高音障害型が半数を占め, 低音障害型, 水平型が次に多く両型で差は認めなかった。初診時と最終時の聴力は, 緩徐型は初診時30～60dB, 最終時では60～80dBに分布し聴力の左右差が少ない症例が多く, 急速型は初診時10～60dB, 最終時50～110dBに広く分布していた。めまいを認めたものは急速型27/51例, 緩徐型17/56例, 複数回繰り返したのは急速型19/51例, 緩徐型14/56例であった。メニエール病鑑別のため急速型でめまいの反復例19例を検討した。初診時聴力型では高音障害型が増加し低音障害型, 水平型は減少した。聴力急性悪化時の周波数域は全周波数域の悪化が多く低音域は少なかった。めまいを伴う特難症例もあると考えた。"}],"abstractLicenseFlag":"disallow"}],"creator":[{"@id":"https://cir.nii.ac.jp/crid/1410001204259899395","@type":"Researcher","personIdentifier":[{"@type":"NRID","@value":"9000000343831"},{"@type":"NRID","@value":"9000253565118"},{"@type":"NRID","@value":"9000254075466"},{"@type":"NRID","@value":"9000254476033"},{"@type":"NRID","@value":"9000019938273"},{"@type":"NRID","@value":"9000254074228"},{"@type":"NRID","@value":"9000254475917"},{"@type":"NRID","@value":"9000254070937"},{"@type":"NRID","@value":"9000254474965"}],"foaf:name":[{"@language":"en","@value":"Ono Yuichi"},{"@language":"ja","@value":"小野 雄一"}],"jpcoar:affiliationName":[{"@language":"en","@value":"Tsukui Red Cross Hospital"},{"@language":"ja","@value":"津久井赤十字病院耳鼻咽喉科"}]},{"@id":"https://cir.nii.ac.jp/crid/1410572172450179841","@type":"Researcher","personIdentifier":[{"@type":"NRID","@value":"9000258221182"}],"foaf:name":[{"@language":"en","@value":"Sano Hajime"},{"@language":"ja","@value":"佐野 肇"}],"jpcoar:affiliationName":[{"@language":"en","@value":"Department of Otolaryngology, Kitasato University, School of Medicine"},{"@language":"ja","@value":"北里大学医学部耳鼻咽喉科"}]},{"@id":"https://cir.nii.ac.jp/crid/1410001204840457856","@type":"Researcher","personIdentifier":[{"@type":"NRID","@value":"9000255411346"},{"@type":"NRID","@value":"9000254478848"},{"@type":"NRID","@value":"9000258220971"},{"@type":"NRID","@value":"9000258220539"},{"@type":"NRID","@value":"9000254075464"},{"@type":"NRID","@value":"9000258221055"},{"@type":"NRID","@value":"9000258220174"},{"@type":"NRID","@value":"9000258220549"},{"@type":"NRID","@value":"9000254479124"},{"@type":"NRID","@value":"9000258221171"},{"@type":"NRID","@value":"9000258221051"},{"@type":"NRID","@value":"9000258221183"},{"@type":"NRID","@value":"9000254478114"},{"@type":"NRID","@value":"9000019938271"},{"@type":"NRID","@value":"9000254479750"},{"@type":"NRID","@value":"9000258220500"},{"@type":"NRID","@value":"9000254075094"},{"@type":"NRID","@value":"9000254479966"},{"@type":"NRID","@value":"9000254075262"},{"@type":"NRID","@value":"9000254075627"}],"foaf:name":[{"@language":"en","@value":"Kamijou 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Medicine"},{"@language":"ja","@value":"北里大学医学部耳鼻咽喉科"}]},{"@id":"https://cir.nii.ac.jp/crid/1410001204840457857","@type":"Researcher","personIdentifier":[{"@type":"NRID","@value":"9000255411370"},{"@type":"NRID","@value":"9000258220968"},{"@type":"NRID","@value":"9000258220538"},{"@type":"NRID","@value":"9000254075467"},{"@type":"NRID","@value":"9000258221058"},{"@type":"NRID","@value":"9000258220175"},{"@type":"NRID","@value":"9000258220548"},{"@type":"NRID","@value":"9000258221174"},{"@type":"NRID","@value":"9000257918800"},{"@type":"NRID","@value":"9000258221052"},{"@type":"NRID","@value":"9000258221184"},{"@type":"NRID","@value":"9000254479753"},{"@type":"NRID","@value":"9000254075093"},{"@type":"NRID","@value":"9000257920314"},{"@type":"NRID","@value":"9000254075101"},{"@type":"NRID","@value":"9000254479967"},{"@type":"NRID","@value":"9000254075263"},{"@type":"NRID","@value":"9000254075628"}],"foaf:name":[{"@language":"en","@value":"Ino Takesi"},{"@language":"ja","@value":"猪 健志"}],"jpcoar:affiliationName":[{"@language":"en","@value":"Department of Otolaryngology, Kitasato University, School of Medicine"},{"@language":"ja","@value":"北里大学医学部耳鼻咽喉科"}]},{"@id":"https://cir.nii.ac.jp/crid/1410001204428504832","@type":"Researcher","personIdentifier":[{"@type":"NRID","@value":"9000258220537"},{"@type":"NRID","@value":"9000014141612"},{"@type":"NRID","@value":"9000258221059"},{"@type":"NRID","@value":"9000258220547"},{"@type":"NRID","@value":"9000258221175"},{"@type":"NRID","@value":"9000258221053"},{"@type":"NRID","@value":"9000258221185"},{"@type":"NRID","@value":"9000258220499"}],"foaf:name":[{"@language":"en","@value":"Makino Hiroyuki"},{"@language":"ja","@value":"牧野 寛之"}],"jpcoar:affiliationName":[{"@language":"en","@value":"Department of Otolaryngology, Kitasato University, School of 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Makito"},{"@language":"ja","@value":"岡本 牧人"}],"jpcoar:affiliationName":[{"@language":"en","@value":"Department of Otolaryngology, Kitasato University, School of Medicine"},{"@language":"ja","@value":"北里大学医学部耳鼻咽喉科"}]}],"publication":{"publicationIdentifier":[{"@type":"PISSN","@value":"03038106"},{"@type":"EISSN","@value":"18837301"},{"@type":"NCID","@value":"AN00000347"}],"prism:publicationName":[{"@language":"en","@value":"AUDIOLOGY JAPAN"},{"@language":"ja","@value":"ＡＵＤＩＯＬＯＧＹ　ＪＡＰＡＮ"},{"@language":"en","@value":"AUDIOLOGY JAPAN"},{"@language":"ja","@value":"ＡＵＤＩＯＬＯＧＹ　ＪＡＰＡＮ"}],"dc:publisher":[{"@language":"en","@value":"Japan Audiological Society"},{"@language":"ja","@value":"一般社団法人 日本聴覚医学会"}],"prism:publicationDate":"2010","prism:volume":"53","prism:number":"2","prism:startingPage":"142","prism:endingPage":"149"},"reviewed":"false","url":[{"@id":"https://search.jamas.or.jp/link/ui/2010194884"}],"availableAt":"2010","foaf:topic":[{"@id":"https://cir.nii.ac.jp/all?q=%E6%80%A5%E9%80%9F%E5%9E%8B","dc:title":"急速型"},{"@id":"https://cir.nii.ac.jp/all?q=%E7%B7%A9%E5%BE%90%E5%9E%8B","dc:title":"緩徐型"},{"@id":"https://cir.nii.ac.jp/all?q=%E3%82%81%E3%81%BE%E3%81%84","dc:title":"めまい"},{"@id":"https://cir.nii.ac.jp/all?q=%E3%83%A1%E3%83%8B%E3%82%A8%E3%83%BC%E3%83%AB%E7%97%85","dc:title":"メニエール病"}],"relatedProduct":[{"@id":"https://cir.nii.ac.jp/crid/1361699994179145856","@type":"Article","relationType":["references"],"jpcoar:relatedTitle":[{"@value":"Terrestrial optical aperture synthesis technique (TOAST)"}]},{"@id":"https://cir.nii.ac.jp/crid/1390001204261380608","@type":"Article","relationType":["references","cites"],"jpcoar:relatedTitle":[{"@language":"en","@value":"Long-Term Observation of Idiopathic Bilateral Sensorineural Hearing Loss."},{"@value":"特発性両側性感音難聴の長期経過観察例　難聴の進行様式と進行速度に関する考察"}]},{"@id":"https://cir.nii.ac.jp/crid/1390001205006291584","@type":"Article","resourceType":"学術雑誌論文(journal article)","relationType":["references"],"jpcoar:relatedTitle":[{"@language":"en","@value":"Vestibular function in bilateral idiopathic progressive sensorineural hearing loss."},{"@value":"特発性両側性感音難聴　とくに前庭機能について"}]},{"@id":"https://cir.nii.ac.jp/crid/1390001205012260352","@type":"Article","resourceType":"学術雑誌論文(journal article)","relationType":["references"],"jpcoar:relatedTitle":[{"@language":"en","@value":"HEARING DISTRIBUTION OF IDIOPATHIC BILATERAL SENSORINEURAL HEARING LOSS"},{"@value":"特発性両側性感音難聴の聴力像"}]},{"@id":"https://cir.nii.ac.jp/crid/1390001205012336640","@type":"Article","resourceType":"学術雑誌論文(journal article)","relationType":["references","cites"],"jpcoar:relatedTitle":[{"@language":"en","@value":"THE EFFECT OF AGING ON OBSERVATION IN HEARING IN THE SAME INDIVIDUALS OVER A 5 YEAR PERIOD"},{"@value":"同一個人の5年間の聴力経過からみた加齢変化"}]},{"@id":"https://cir.nii.ac.jp/crid/1390001205012674688","@type":"Article","resourceType":"学術雑誌論文(journal article)","relationType":["references"],"jpcoar:relatedTitle":[{"@language":"en","@value":"IDIOPATHIC BILATERAL SENSORINEURAL HEARING LOSS"},{"@value":"特発性両側性感音難聴の検討"}]},{"@id":"https://cir.nii.ac.jp/crid/1390282679239789312","@type":"Article","relationType":["cites"],"jpcoar:relatedTitle":[{"@language":"en","@value":"Epidemiological and Clinical Survey on Definite Cases of Bilateral Meniere's Disease as Reported by Seventeen Members of Meniere's Disease Research Committee of Japan During 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