A case of retroperitoneal malignant peripheral nerve sheath tumor in a patient with neurofibromatosis

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  • 神経線維腫症I型患者に合併した後腹膜悪性末梢神経鞘腫の1例
  • 症例 神経線維腫症1型患者に合併した後腹膜悪性末梢神経鞘腫の1例
  • ショウレイ シンケイ センイ シュショウ 1ガタ カンジャ ニ ガッペイ シタ コウフク マク アクセイ マッショウ シンケイショウ シュ ノ 1レイ

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Abstract

We report a case of retroperitoneal malignant peripheral nerve sheath tumor (MPNST) in a patient with neurofibromatosis 1. A 42-year-old woman was admitted because of a palpable left abdominal mass. Her mother, son, and daughter had neurofibromatosis 1. Computed tomography and magnetic resonance imaging revealed a 73 x 76 mm retroperitoneal mass. We performed complete resection of the tumor, confirming the margin status by frozen section examination intraoperatively. The histopathological examination revealed MPNST. Although no further therapy was performed, she is alive with no evidence of disease 11 months after surgery.

Journal

  • Hinyokika Kiyo

    Hinyokika Kiyo 52 (3), 207-209, 2006-03

    泌尿器科紀要刊行会

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