Bilateral Pleural Effusions as an Initial Presentation in Primary Sjögren’s Syndrome

  • Go Makimoto
    Department of Respiratory Medicine, Okayama Rosai Hospital, 1-10-25 Chikkomidorimachi, Minami-ku, Okayama 7028055, Japan
  • Michiko Asano
    Department of Respiratory Medicine, Okayama Rosai Hospital, 1-10-25 Chikkomidorimachi, Minami-ku, Okayama 7028055, Japan
  • Nobukazu Fujimoto
    Department of Respiratory Medicine, Okayama Rosai Hospital, 1-10-25 Chikkomidorimachi, Minami-ku, Okayama 7028055, Japan
  • Yasuko Fuchimoto
    Department of Respiratory Medicine, Okayama Rosai Hospital, 1-10-25 Chikkomidorimachi, Minami-ku, Okayama 7028055, Japan
  • Katsuichiro Ono
    Department of Respiratory Medicine, Okayama Rosai Hospital, 1-10-25 Chikkomidorimachi, Minami-ku, Okayama 7028055, Japan
  • Shinji Ozaki
    Department of Respiratory Medicine, Okayama Rosai Hospital, 1-10-25 Chikkomidorimachi, Minami-ku, Okayama 7028055, Japan
  • Koji Taguchi
    Department of Pathology, Okayama Rosai Hospital, 1-10-25 Chikkomidorimachi, Minami-ku, Okayama 7028055, Japan
  • Takumi Kishimoto
    Department of Respiratory Medicine, Okayama Rosai Hospital, 1-10-25 Chikkomidorimachi, Minami-ku, Okayama 7028055, Japan

書誌事項

公開日
2012
権利情報
  • http://creativecommons.org/licenses/by/3.0/
DOI
  • 10.1155/2012/640353
公開者
Wiley

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説明

<jats:p>Sjögren’s syndrome (SS) is a systemic autoimmune disease characterized by sicca symptoms. Interstitial pulmonary fibrosis and tracheobronchial sicca are the most common symptoms of pulmonary involvement in primary SjS, and they are rarely accompanied by serositis such as pleuritis or pericarditis. We report a case of SS presenting initially with bilateral pleural effusions. A 63-year old man was admitted to our hospital with a one-month history of cough, dyspnea, and right chest pain. Chest-computed tomography revealed bilateral pleural effusions. Serum anti-SS-A antibody titer was 1 : 256. Ophthalmological examination revealed a positive Schirmer test. Lip biopsy showed atrophy and plasmacytic infiltration of the salivary gland. Corticosteroid treatment was initiated. Pleural effusions were almost completely resolved by day 30. The patient has not experienced any recurrence.</jats:p>

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