α-L-Iduronidass Activity in Established Lymphoblastoid Cells from Patients with Hurler and Scheie Syndromes Transformed by Epstein-Barr Virus
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- MINAMI RYOJI
- Department of Pediatrics, Sapporo Medical College
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- SUZUKI MASAHIRO
- Department of Pediatrics, Sapporo Medical College
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- KUDOH TOORU
- Department of Pediatrics, Sapporo Medical College
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- SATO SIGEO
- Department of Pediatrics, Sapporo Medical College
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- OYANAGI KAZUHIKO
- Department of Pediatrics, Sapporo Medical College
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- NAKAO TOORU
- Department of Pediatrics, Sapporo Medical College
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- SUKEGAWA KAZUKO
- Department of Pediatrics, Gifu University School of Medicine
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- ORII TADAO
- Department of Pediatrics, Gifu University School of Medicine
書誌事項
- タイトル別名
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- .ALPHA.-L-Iduronidase activity in established lymphoblastoid cells from patients with hurler and scheie syndromes transformed by epstein-barr virus.
- アルファ L Iduronidass Activity in Establis
この論文をさがす
抄録
α-L-Iduronidase activity was determined in established lymphoblastoid cells, which were transformed in vitro by Epstein-Barr virus, of lymphocytes-rich cell populations isolated from peripheral blood of patients with Hurler and Scheie syndromes. α-L-Iduronidase activities in established lymphoblastoid cells from patients were undetectable, while activities of control subjects were clearly detected. These results suggest that established lymphoblastoid cells are useful for the enzymatic study of genetic mucopolysaccharidoses.
収録刊行物
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- The Tohoku Journal of Experimental Medicine
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The Tohoku Journal of Experimental Medicine 122 (4), 393-396, 1977
東北ジャーナル刊行会
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キーワード
詳細情報 詳細情報について
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- CRID
- 1390001204239646976
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- NII論文ID
- 130003492342
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- NII書誌ID
- AA00863920
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- COI
- 1:STN:280:DyaE1c%2FjsVOqsQ%3D%3D
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- ISSN
- 13493329
- 00408727
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- NDL書誌ID
- 1912566
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- PubMed
- 199964
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- 本文言語コード
- en
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- データソース種別
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- JaLC
- NDL
- Crossref
- PubMed
- CiNii Articles
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- 抄録ライセンスフラグ
- 使用不可