Two Cases of Proteus Syndrome Characterized by Verrucous Skin Lesions on the Soles.

DOI 1 Citations 6 References

Bibliographic Information

Other Title
  • 足底に典型的なゆう状腫りゅうを呈したプロテウス症候群の２例

Description

Proteus syndrome is an extremely rare, complex hamartomatous syndrome that consists of either partial or complete hemihypertrophy, macrodactyly of the hands and/or feet, plantar hyperplasia, hemangiomas, lipomas, lymphangiomas, varicosities, verrucous epidermal nevi, cranial hyperostoses and long-bone overgrowth. The syndrome was named after the Greek god Proteus (the polymorphous God who could change his shape at will to avoid capture) by Wiedemann et al in 1983. We report 2 cases of Proteus syndrome. They were a 13-year-old boy and a 37-year-old woman, presenting connective tissue nevi-like verrucous tumors on the soles. In the latter case, the hamartomatous lesions were only detected by an intensive systemic examination because of the relatively mild associated symptoms. We also discuss the variations of the extent of major and minor clinical features of this syndrome in our cases.

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Details 詳細情報について

  • CRID
    1390001204298208000
  • NII Article ID
    130004473823
  • DOI
    10.2336/nishinihonhifu.54.1067
  • ISSN
    18804047
    03869784
    http://id.crossref.org/issn/00225347
  • Text Lang
    ja
  • Data Source
    • JaLC
    • Crossref
    • CiNii Articles
  • Abstract License Flag
    Disallowed

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