A Case of Acropathies Ulcéro-Mutilantes Pseudo-Syringomyéliques non Familiales des Membres Inférieurs

WADA Hidetoshi, TAKEISHI Masaaki

doi:10.2336/nishinihonhifu.42.953

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Acropathies Ulcéro-Mutilantes Pseudo-Syringomyéliques non Familiales des Membres Inférieursの1例
Acropathies Ulcero-Mutilantes Pseudo-Syringomyeliques non Familiales des Membres Inferieursの1例
Acropathies Ulcero Mutilantes Pseudo Sy
Ａｃｒｏｐａｔｈｉｅｓ　Ｕｌｃｅ´ｒｏ‐Ｍｕｔｉｌａｎｔｅｓ　Ｐｓｅｕｄｏ‐Ｓｙｒｉｎｇｏｍｙｅ´ｌｉｑｕｅｓ　ｎｏｎ　Ｆａｍｉｌｉａｌｅｓ　ｄｅｓ　Ｍｅｍｂｒｅｓ　Ｉｎｆｅ´ｒｉｅｕｒｓの一例

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A case of acropathies ulcéro-mutilantes pseudo-syringomyéliques non familiales des membres inférieurs in a 56-year-old public official was reported. The patient was admitted with a marked swelling and deformity of the right big toe and recurrent ulcer surrounded by tylosis-like keratosis on the sole. Within the following years the patient was hospitalized 3 times, the ulcer was removed and covered with a full thickness skin graft several times. The graft was always not stable in consequence of a recurrent ulceration. At the last admission the big toe was amputated because of a macrodactylia-like deformity with ulcer. This disease is characterized by chronic ulceration as a result of slight injury, neurogenic acro-osteolysis, sensory disturbance of the extremities and is of a non-familial incidence. This disease usually begins in middle aged men who are undernourished as the result of chronic alcohol ingestion. Such cases have been reported in France, but this is the first typical case to be documented in Japan.

Journal

Nishi Nihon Hifuka

Nishi Nihon Hifuka 42 (6), 953-957, 1980

Western Division of Japanese Dermatological Association

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