Realignment and Intramedullary Rod Fixation for Osteogenesis Imperfecta. A Case Report.

DOI

Bibliographic Information

Other Title
  • 両側大腿骨および両側けい骨に矯正骨切り術を行った骨形成不全症の１例
  • A Case Report

Abstract

We performed corrective multiple osteotomy and intramedullary rod fixation on the bilateral femora and tibiae of a 4-year-old boy with osteogenesis imperfecta (OI) who had marked locomotive disturbance resulting from fragility and deformity of the lower limbs. Nailing was performed with a 3.2mm diameter telescoping rod for the right femur, and with a 3mm diameter Kirschner's wire for the left femur and both tibiae. Forward flexure of the right tibia subsequently recurred, resulting in cutting of the tibia by the Kirschner's wire. Reoperation was thus required. One year and 8 months after the reoperation, the patient is able to maintain a standing position and has acquired some locomotive capability.<br>Children with OI who often have a history of fractures, tend to limit their movement in order to reduce the possibility of sustaining additional fractures. This results in disuse atrophy and fragility of the extremities, and ultimately severe locomotive disturbance. In the present case, invasive treatment reduced the risk of francture. The patient can now perform exercises including kneeling, and these exercises can be expected to further improve his clinical condition.

Journal

Keywords

Details 詳細情報について

  • CRID
    1390001204349338368
  • NII Article ID
    130003437526
  • DOI
    10.11360/jcsoa1989.6.459
  • ISSN
    13475606
    09152695
  • Text Lang
    ja
  • Data Source
    • JaLC
    • CiNii Articles
  • Abstract License Flag
    Disallowed

Report a problem

Back to top