Malformation of the Atrial Septum with Hemodynamic Equivalence to Partial Anomalous Pulmonary Venous Connection and Difficult Differentiation from Cor Triatriatum in an Infant
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- Yamashiro Masahito
- Department of Cardiac Surgery, The Jikei University
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- Morita Kiyozo
- Department of Cardiac Surgery, The Jikei University
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- Uno Yoshimasa
- Department of Cardiac Surgery, The Jikei University
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- Ko Yoshihiro
- Department of Cardiac Surgery, The Jikei University
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- Muramatsu Koichi
- Department of Cardiac Surgery, The Jikei University
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- Hashimoto Kazuhiro
- Department of Cardiac Surgery, The Jikei University
Bibliographic Information
- Other Title
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- 血行動態的に部分肺静脈還流異常を呈した心房中隔形成異常の幼児手術例:非定型的三心房心との鑑別
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Description
Partial anomalous pulmonary venous connection is a relatively common congenital heart defect. Cor triatriatum is a rare congenital heart anomaly that typically result in congestive heart failure due to pulmonary venous obstruction. Discrimination between an anomalous pulmonary venous connection and cor triatriatum is important for surgical treatment; however, an accurate diagnosis is sometimes difficult. We surgically corrected an atrial septal malformation with hemodynamic equivalence to partial anomalous pulmonary venous connection in an infant. Discrimination was difficult between this combination and cor triatriatum combined with malformation of the atrial septum primum and secundum. Echocardiography and cardiac catheterization did not provide sufficient information on intracardiac structures. Preoperative 3D-CT was useful for anatomical diagnosis and determination of the surgical septation line.
Journal
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- Pediatric Cardiology and Cardiac Surgery
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Pediatric Cardiology and Cardiac Surgery 28 (1), 48-53, 2012
Japanese Society of Pediatric Cardiology and Cardiac Surgery
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Details 詳細情報について
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- CRID
- 1390001204670761600
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- NII Article ID
- 10030648965
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- NII Book ID
- AN10042853
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- ISSN
- 21872988
- 09111794
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- Text Lang
- ja
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- Data Source
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- JaLC
- Crossref
- CiNii Articles
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- Abstract License Flag
- Disallowed