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- Ohmichi Shiro
- Department of Pedodontics, Osaka Dental University
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- Kawahara Shigeru
- Department of Pedodontics, Osaka Dental University
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- Kato Mikio
- Department of Pedodontics, Osaka Dental University
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- Takahara Toshiyuki
- Department of Pedodontics, Osaka Dental University
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- Ozaki Sadanobu
- Department of Pedodontics, Osaka Dental University
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- Daito Michiharu
- Department of Pedodontics, Osaka Dental University
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- Hieda Toyoji
- Department of Pedodontics, Osaka Dental University
Bibliographic Information
- Other Title
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- 骨形成不全症の1症例について
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Abstract
Osteogenesis imperfecta (OGI) is a rare genetic disease which, as a result of a disorder in the formation of the organic stroma of the bone due to a defect in osteogenic function, induces brittle bones, whereby only weak forces bring about multiple, repeated pathological fractures.<BR>This disease is thought to entail various problems with regards to carrying out pediatric dentistry due to the ease with which bones may be fractured.<BR>We report here the findings obtained as a result of the careful examination of a 1-year-3-month-old girl encountered in our practice and who was diagnosed as having osteogenesis imperfecta.<BR>1) Out of the three major symptoms for osteogenesis imperfecta, this case showed signs of fragile bones and blue scleras, but did not reveal signs of deafness.<BR>2) There was retardation in system growth and development.<BR>3) Aside from a high level of alkaline phosphatase, there were no notable abnormalities revealed in the biochemical blood tests.<BR>4) Dentinogenesis imperfecta was observed throughout the erupted teeth.<BR>5) There was a definite improvement in cooperation with each visit to the clinic.
Journal
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- The Japanese Journal of Pediatric Dentistry
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The Japanese Journal of Pediatric Dentistry 28 (3), 720-724, 1990
The Japanese Society of Pediatric Dentistry