An autopsy case of intrahepatic cholangiocarcinoma associated with neurofibromatosis type 1 (von Recklinghausen's disease)
-
- Koyanagi Toshimasa
- Department of Hepatology, Iizuka Hospital
-
- Masumoto Akihide
- Department of Hepatology, Iizuka Hospital
-
- Tajiri Hirotaka
- Department of Hepatology, Iizuka Hospital
-
- Yada Masayoshi
- Department of Hepatology, Iizuka Hospital
-
- Senjyu Takeshi
- Department of Hepatology, Iizuka Hospital
-
- Motomura Kenta
- Department of Hepatology, Iizuka Hospital
-
- Oya Masafumi
- Department of Pathology, Iizuka Hospital
Bibliographic Information
- Other Title
-
- 神経線維腫症1型(von Recklinghausen病)に合併した肝内胆管癌の1剖検例
- 症例報告 神経線維腫症1型(von Recklinghausen病)に合併した肝内胆管癌の1剖検例
- ショウレイ ホウコク シンケイ センイ シュショウ 1ガタ(von Recklinghausenビョウ)ニ ガッペイ シタ カン ナイタンカンガン ノ 1 ボウケンレイ
Search this article
Abstract
A 69-year old man, who had neurofibromatosis type 1 (von Recklinghausen's disease), was referred to our hospital because of a symptom of persistent abdominal fullness. The extensive examinations revealed huge hepatic mass in the left lobe, suggesting a diagnosis of intrahepatic cholangiocarcinoma. One month later, the patient showed a rapid progress of anemia and bloody ascites suggestive of tumor rupture. Hepatic anteriography showed a large heterogeneous tumor in the left lateral lobe and transcathetel arterial embolization was performed. However, the patient died from hepato-renal failure. An autopsy revealed moderately-differentiated intrahepatic cholangiocarcinoma with necrosis and vascular invasion, metastasizing to the lungs, hilar lymph nodes, parietal pleura, right kidney, perisplenic fat, and adrenal glands. Intrahepatic cholangiocarcinoma associated with neurofibromatosis type 1 is rare.<br>
Journal
-
- Kanzo
-
Kanzo 53 (4), 231-236, 2012
The Japan Society of Hepatology
- Tweet
Keywords
Details 詳細情報について
-
- CRID
- 1390001204793876992
-
- NII Article ID
- 130002098008
- 10030625444
-
- NII Book ID
- AN00047770
-
- ISSN
- 18813593
- 04514203
-
- NDL BIB ID
- 023602428
-
- Text Lang
- ja
-
- Data Source
-
- JaLC
- NDL
- Crossref
- CiNii Articles
-
- Abstract License Flag
- Disallowed