Incomplete Testicular Feminization Syndrome : Report of A Case

DOI 11 References
  • Matsuzaki Shigeru
    Division of Pediatric Surgery, Jichi Medical School:Department of Surgery, Jichi Medical School
  • Makino Shun-Ichi
    Division of Pediatric Surgery, Jichi Medical School:Department of Surgery, Jichi Medical School
  • Itoh Mitsuhiro
    Division of Pediatric Surgery, Jichi Medical School:Department of Surgery, Jichi Medical School
  • Uchida Hiroo
    Division of Pediatric Surgery, Jichi Medical School:Department of Surgery, Jichi Medical School
  • Nokubi Mitsuhiro
    Department of Pathology, Jichi Medical School
  • Matsumoto Seiichi
    Department of Obstetrics & Gynecology, Jichi Medical School

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  • 不完全型精巣性女性化症候群を呈した男性仮性半陰陽の1学童例

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A 46, XY individual with incomplete testicular feminization syndrome was investigated. The patient's chief complaints were clitoromegaly and inguinal nodules. The hormonal studies showed high serum testosterone(T) and FSH. The dihydrotestosterone(DHT) level was relatively low. The ratio of T:DHT was slightly high, 22. After stimulation with hCG. both T and DHT responded well, and the ratio decreased to 17. The radiological and surgical examinations revealed that inguinal nodules were testicles and there were epididymis and vas deferens. Mullerian derivatives and ovaries did not exist. The gonads were resected, and subtunical total reduction clitoroplasty was carried out. Pathological examinations of testicles showed that atrophic seminiferous tubles were populated by Sertoli cells without spermatocytes. Leydig cells were rich in number. "She" received estrogen for further feminization.

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