A case of Wegener's granulomatosis showing a dramatic response to corticosteroid and cyclophosphamide therapy

  • HIRANO KIYOSHI
    Division of Nephrology, Department of Internal Medicine, Juntendo University School of Medicine
  • TOMINO YASUHIKO
    Division of Nephrology, Department of Internal Medicine, Juntendo University School of Medicine
  • MURAI TOSHIO
    Division of Nephrology, Department of Internal Medicine, Juntendo University School of Medicine
  • WANG LI NING
    Division of Nephrology, Department of Internal Medicine, Juntendo University School of Medicine
  • SHIRATO ISAO
    Division of Nephrology, Department of Internal Medicine, Juntendo University School of Medicine
  • KOIDE HIKARU
    Division of Nephrology, Department of Internal Medicine, Juntendo University School of Medicine

Bibliographic Information

Other Title
  • —Evaluation of anticytoplasmic antibodies (ACPA) in serum samples—

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Description

A case of Wegener's granulomatosis with renal dysfunction is described. Granulomatous lesions of the lung, left eyelid and left leg, and chronic sinusitis were observed at the time of admission. Renal and skin biopsy specimens revealed typical features of Wegener's granulomatosis on light microscopy and immuno fluorescence microscopy. A dramatic response occurred following cortico steroid and cyclophosphamide therapy, characterized by improvement of proteinuria and renal function, and disappearance of the granulomas and 67gallium citrate accumulations in both the eyes and nose. Further-more, the levels of anticytoplasmic antibodies (ACPA) in the serum samples were significantly decreased after such therapy. It appears that combined therapy with corticosteroid and cyclophosphamide can be effective in improving proteinuria and renal dysfunction, and in reducing of ACPA in patients with Wegener's granulomatosis.

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Details 詳細情報について

  • CRID
    1390001204860750080
  • NII Article ID
    130004169690
  • DOI
    10.14842/jpnjnephrol1959.32.339
  • ISSN
    18840728
    03852385
  • PubMed
    2355667
  • Text Lang
    en
  • Article Type
    journal article
  • Data Source
    • JaLC
    • PubMed
    • CiNii Articles
  • Abstract License Flag
    Disallowed

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