Advanced Hirayama Disease with Successful Improvement of Activities of Daily Living by Operative Reconstruction
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- CHIBA Susumu
- Department of Neurology, School of Medicine, Sapporo Medical University
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- YONEKURA Kazumi
- Department of Neurology, School of Medicine, Sapporo Medical University
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- NONAKA Michio
- Department of Neurology, School of Medicine, Sapporo Medical University
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- IMAI Tomihiro
- Department of Neurology, School of Medicine, Sapporo Medical University
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- MATUMOTO Hiroyuki
- Department of Neurology, School of Medicine, Sapporo Medical University
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- WADA Takuro
- Department of Orthopaedic Surgery, School of Medicine, Sapporo Medical University
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Description
Juvenile muscular atrophy of the distal upper extremity (Hirayama disease) is a benign and non-progressive motor neuron disease. Application of a cervical collar is believed to prevent progression of symptoms in the early stages, but there is no effective therapy for the advanced disease. We found that tendon transfer improved the activities of daily living (ADL) of a patient with advanced Hirayama disease. An operative reconstruction can be valuable, even in patients with Hirayama disease who have developed impaired ADL due to extensive intrinsic hand muscle atrophy.
Journal
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- Internal Medicine
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Internal Medicine 43 (1), 79-81, 2004
The Japanese Society of Internal Medicine
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Details 詳細情報について
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- CRID
- 1390001204867147008
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- NII Article ID
- 130000083978
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- NII Book ID
- AA10827774
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- ISSN
- 13497235
- 09182918
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- NDL BIB ID
- 6828878
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- PubMed
- 14964585
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- Text Lang
- en
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- Data Source
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- JaLC
- NDL
- Crossref
- PubMed
- CiNii Articles
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- Abstract License Flag
- Disallowed