A Case of Neurofibromatosis Type 1 with Multiple Rectal Carcinoids
-
- Yamaguchi Takashi
- Department of Surgery, National Hospital Organization Kyoto Medical Center
-
- Minamiguchi Sachiko
- Department of Pathology, National Hospital Organization Kyoto Medical Center
-
- Yamato Toshio
- Department of Surgery, National Hospital Organization Kyoto Medical Center
-
- Uehiro Natsue
- Department of Surgery, National Hospital Organization Kyoto Medical Center
-
- Hata Hiroaki
- Department of Surgery, National Hospital Organization Kyoto Medical Center
-
- Ogiso Satoshi
- Department of Surgery, National Hospital Organization Kyoto Medical Center
-
- Otani Tetsushi
- Department of Surgery, National Hospital Organization Kyoto Medical Center
-
- Tsuchiya Nobuyuki
- Department of Surgery, National Hospital Organization Kyoto Medical Center
-
- Koizumi Kinya
- Department of Surgery, National Hospital Organization Kyoto Medical Center
Bibliographic Information
- Other Title
-
- 多発性直腸カルチノイドを合併した神経線維腫症1型の1例
Search this article
Description
A 43-year-old woman with neurofibromatosis type 1 (NF1) reporting hematochezia was found in colonoscopy to have a few small submucosal nodules in the lower rectum, confirmed from a locally resected specimen to be carcinoid tumor. Abdominal computed tomography (CT) showing a 3 cm mass in the rectal posterior wall and a 3.5 cm mass in the ileocolic mesentery, necessitated low anterior rectum resection and ileocolic tumor excision. Histological diagnosis showed both tumors to be plexiform neurofibromas. Ten carcinoids 1 to 6 mm in diameter were found in the resected rectum with lymph-node metastasis. In patients with NF1, neurofibromas may be present in the abdominal cavity. Carcinoid tumors may arise in the periampullary area but rarely in the rectum. We present a case with NF1 accompanying abdominal plexiform neurofibromas and multiple rectal carcinoids.
Journal
-
- The Japanese Journal of Gastroenterological Surgery
-
The Japanese Journal of Gastroenterological Surgery 43 (2), 202-207, 2010
The Japanese Society of Gastroenterological Surgery
- Tweet
Keywords
Details 詳細情報について
-
- CRID
- 1390001204919435776
-
- NII Article ID
- 110007539276
-
- NII Book ID
- AN00192066
-
- ISSN
- 13489372
- 03869768
- http://id.crossref.org/issn/03869768
-
- Text Lang
- ja
-
- Data Source
-
- JaLC
- Crossref
- CiNii Articles
-
- Abstract License Flag
- Disallowed