Neck infection with Kostmann syndrome
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- Yoshie Urara
- Division of Otolaryngology, Chiba Children's Hospital
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- Arimoto Yukiko
- Division of Otolaryngology, Chiba Children's Hospital
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- Nakano Atsuko
- Division of Otolaryngology, Chiba Children's Hospital
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- Kudo Fumiyo
- Department of Nutrition Faculty of Health Care Science, Chiba Prefectural University of Health Sciences
Bibliographic Information
- Other Title
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- 喉頭浮腫を呈した Kostmann 症候群の一例
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Abstract
“Neutropenia” generally indicates a blood pathology in which the concentration of neutrophils in the peripheral blood is lower than 1500/mm3. Kostmann syndrome is a rare congenital severe neutropenia and is characterized by recurrent bacterial infections, fever, skin infection, gingivitis and early life-threatening infections. We report a 6–year-old girl with Kostmann syndrome who suffered from neck infection and swelling in the epiglottis without pain. She needed a daily dose of antibiotics to prevent infection. She visited to our hospital complaining of a cough. Four days after the visit, she started to experience fever and hoarseness, and one week after the visit, she returned with a right submandibular mass. Computed tomography revealed a low attenuation mass in the right parapharyngeal space without ring enhancement. A fexible laryngoscope study revealed swelling in the epiglottis and right arytenoid cartilag. Based on these findings the patient was diagnosed with a deep neck infection, and intravenous administration of antibiotics (meropenem), steroid and G–CSF (granulocyte colony-stimulating factor) was started immediately, following which a gradual improvement insymptoms was observed. However, swelling in the epiglottis remained unchanged.
Journal
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- Pediatric Otorhinolaryngology Japan
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Pediatric Otorhinolaryngology Japan 31 (1), 24-28, 2010
Japan Society for Pediatric Otorhinolaryngology
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Keywords
Details 詳細情報について
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- CRID
- 1390001205465512704
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- NII Article ID
- 130004672161
- 10026419151
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- NII Book ID
- AN10044779
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- ISSN
- 21865957
- 09195858
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- Text Lang
- ja
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- Data Source
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- JaLC
- CiNii Articles
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- Abstract License Flag
- Disallowed