Two Cases of Paroxysmal Nocturnal Hemoglobinuria with Preceding Cytopenia

  • Inamura Junki
    Division of Gastroenterology and Hematology/Oncology, Department of Medicine, Asahikawa Medical University
  • Ikuta Katsuya
    Division of Gastroenterology and Hematology/Oncology, Department of Medicine, Asahikawa Medical University
  • Toki Yasumichi
    Division of Gastroenterology and Hematology/Oncology, Department of Medicine, Asahikawa Medical University
  • Hatayama Mayumi
    Division of Gastroenterology and Hematology/Oncology, Department of Medicine, Asahikawa Medical University
  • Ito Satoshi
    Division of Gastroenterology and Hematology/Oncology, Department of Medicine, Asahikawa Medical University
  • Shindo Motohiro
    Division of Gastroenterology and Hematology/Oncology, Department of Medicine, Asahikawa Medical University
  • Sato Kazuya
    Department of Hematology/Oncology, Asahikawa Kosei Hospital
  • Torimoto Yoshihiro
    Oncology Center, Asahikawa Medical University Hospital
  • Kohgo Yutaka
    Division of Gastroenterology and Hematology/Oncology, Department of Medicine, Asahikawa Medical University

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Other Title
  • 汎血球減少の経過が先行した発作性夜間血色素尿症の2例
  • 今月の症例 汎血球減少の経過が先行した発作性夜間血色素尿症の2例
  • コンゲツ ノ ショウレイ ハンケッキュウ ゲンショウ ノ ケイカ ガ センコウ シタ ホッサセイ ヤカン ケッシキソ ニョウショウ ノ 2レイ

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Abstract

発作性夜間血色素尿症(paroxysmal nocturnal hemoglobinuria:以下PNH)は,補体感受性の亢進した赤血球がクローン性に増殖し,補体活性化に伴い溶血をきたす稀な疾患であり,背景に造血障害を伴うことが多い.当科で経験した2症例においても血球減少がみられたが,その程度や経時的変動には大きな違いがあった.PNH患者の血球数における変動や個人差の原因について考察する.

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