Two Cases of Paroxysmal Nocturnal Hemoglobinuria with Preceding Cytopenia
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- Inamura Junki
- Division of Gastroenterology and Hematology/Oncology, Department of Medicine, Asahikawa Medical University
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- Ikuta Katsuya
- Division of Gastroenterology and Hematology/Oncology, Department of Medicine, Asahikawa Medical University
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- Toki Yasumichi
- Division of Gastroenterology and Hematology/Oncology, Department of Medicine, Asahikawa Medical University
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- Hatayama Mayumi
- Division of Gastroenterology and Hematology/Oncology, Department of Medicine, Asahikawa Medical University
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- Ito Satoshi
- Division of Gastroenterology and Hematology/Oncology, Department of Medicine, Asahikawa Medical University
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- Shindo Motohiro
- Division of Gastroenterology and Hematology/Oncology, Department of Medicine, Asahikawa Medical University
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- Sato Kazuya
- Department of Hematology/Oncology, Asahikawa Kosei Hospital
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- Torimoto Yoshihiro
- Oncology Center, Asahikawa Medical University Hospital
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- Kohgo Yutaka
- Division of Gastroenterology and Hematology/Oncology, Department of Medicine, Asahikawa Medical University
Bibliographic Information
- Other Title
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- 汎血球減少の経過が先行した発作性夜間血色素尿症の2例
- 今月の症例 汎血球減少の経過が先行した発作性夜間血色素尿症の2例
- コンゲツ ノ ショウレイ ハンケッキュウ ゲンショウ ノ ケイカ ガ センコウ シタ ホッサセイ ヤカン ケッシキソ ニョウショウ ノ 2レイ
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Abstract
発作性夜間血色素尿症(paroxysmal nocturnal hemoglobinuria:以下PNH)は,補体感受性の亢進した赤血球がクローン性に増殖し,補体活性化に伴い溶血をきたす稀な疾患であり,背景に造血障害を伴うことが多い.当科で経験した2症例においても血球減少がみられたが,その程度や経時的変動には大きな違いがあった.PNH患者の血球数における変動や個人差の原因について考察する.
Journal
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- Nihon Naika Gakkai Zasshi
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Nihon Naika Gakkai Zasshi 103 (6), 1385-1387, 2014
The Japanese Society of Internal Medicine
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Keywords
Details 詳細情報について
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- CRID
- 1390001206446376960
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- NII Article ID
- 130005075595
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- NII Book ID
- AN00195836
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- ISSN
- 18832083
- 00215384
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- NDL BIB ID
- 025587568
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- Text Lang
- ja
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- Data Source
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- JaLC
- NDL
- Crossref
- CiNii Articles
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- Abstract License Flag
- Disallowed