A Case of Hemophilia B Diagnosed in a Patient Who Presented with Repeated Post-Tonsillectomy Hemorrhage
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- Wakabayashi Tokio
- Kawasaki Medical School
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- Fukuda Yujiro
- Kawasaki Medical School
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- Fukushima Hisaki
- Kawasaki Medical School
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- Fujita Naoaki
- Kawasaki Medical School
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- Hara Hirotaka
- Kawasaki Medical School
Bibliographic Information
- Other Title
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- 口蓋扁桃摘出術後出血を契機に診断された血友病B例
- コウガイ ヘントウ テキシュツジュツ コウシュッケツ オ ケイキ ニ シンダン サレタ ケツユウビョウ Bレイ
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Abstract
<p>Hemophilia B is an X-linked disease characterized by decreased in blood level of coagulation factor IX activity. Mild to moderate hemophilia is often diagnosed only after surgery or trauma. We encountered a case of hemophilia B, in which the diagnosis was made after the patient presented with recurrent postoperative hemorrhage. The patient was a 4-year-old boy without any remarkable past medical history of bleeding disorders. He was diagnosed as having severe obstructive sleep apnea, and underwent adenotonsillectomy under general anesthesia. Postoperative hemorrhage occurred on day 2 and day 6 after surgery, and procedures for hemostasis were required on both days. He exhibited recurrent hemorrhage and showed a prolonged activated partial thromboplastin time of 62.3 s; therefore, we suspected coagulopathy. Further examination revealed a reduced blood coagulation factor IX activity level, and the patient was diagnosed as having moderate hemophilia B. This case indicates the importance of preoperative screening for coagulation defects, especially before tonsillectomy, as post-tonsillectomy bleeding can be fatal.</p>
Journal
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- Practica Oto-Rhino-Laryngologica
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Practica Oto-Rhino-Laryngologica 114 (9), 689-694, 2021
The Society of Practical Otolaryngology
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Details 詳細情報について
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- CRID
- 1390007757214528512
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- NII Article ID
- 130008081953
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- NII Book ID
- AN00107089
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- ISSN
- 18844545
- 00326313
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- NDL BIB ID
- 031700401
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- Text Lang
- ja
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- Data Source
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- JaLC
- NDL
- Crossref
- CiNii Articles
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- Abstract License Flag
- Disallowed