A Case of Ovarian Sex Cord Tumor With Annular Tubules (SCTAT) in Which Fertility Was Preserved

Ueno Yuri, Ohtsu Kazuhiro, Kamei Naomi

doi:10.11164/jjsps.57.6_959

Bibliographic Information

Other Title

妊孕性を温存し得た卵巣の輪状細管を伴う性索腫瘍（SCTAT）の1女児例
ニンヨウセイオオンゾンシエタランソウノリンジョウサイカンオトモナウセイサクシュヨウ(SCTAT)ノ 1 ジョジレイ

Search this article

Abstract

<p>Sex cord tumor with annular tubules (SCTAT) is a rare borderline malignant tumor compared with other sex cord-stromal tumors. This tumor often produces female sex hormones and is known to complicate Peutz-Jeghers syndrome (PJS). The patient was a girl aged 9 years and 6 months who was brought to our hospital presenting with chief complaints of breast enlargement and atypical genital bleeding. An approximately 11-cm serous cystic lesion was present in the left ovary and the serum estradiol (E2) level was high. The lesion temporarily shrank and the E2 level also decreased during the course of observation, but the lesion re-enlarged thereafter. Suspecting a reactive ovarian cyst, we performed partial ovarian cystectomy and the lesion was histopathologically diagnosed as SCTAT. No standard treatment for SCTAT has been established. In this patient, to preserve fertility, adnexectomy was performed only on the affected side seven months after partial ovarian cystectomy. Since the patient’s case was not complicated by PJS and it has been reported that about 20% of noncomplicated cases follow a malignant course, a strict course of observation will be necessary hereafter.</p>

Journal

Journal of the Japanese Society of Pediatric Surgeons

Journal of the Japanese Society of Pediatric Surgeons 57 (6), 959-964, 2021-10-20

The Japanese Society of Pediatric Surgeons

Keywords

Details 詳細情報について

Export