Renal Lesions in Cockayne's Syndrome
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- Ohno Tadasi
- Department of Pediatrics, Akita Central Hospital
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- Hirooka Minoru
- Department of Pediatrics, Akita Central Hospital
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Abstract
Three males, 4 years, 6 years and 5 years of age, with typical Cockayne's syndrome were described.<br> Differential diagnostic criteria between Cockayne's syndrome and progeria were discussed and the authors were of the opinion that the two syndromes represented two different disease entities.<br> Histologic findings of the kidney biopsied in 2 cases with this syndrome revealed thickening of glomerular basement membrane and mesangium, collapse or atrophy of capillary loops, hyalinization of glomeruli, atrophy of tubules, thickening of the basement membrane of atrophic tubules and interstitial fibrosis. These renal lesions have not been reported so far in Cockayne's syndrome. In this respect, possible relationships between Cockayne's syndrome and so-called hereditary nephropathy were discussed.
Journal
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- The Tohoku Journal of Experimental Medicine
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The Tohoku Journal of Experimental Medicine 89 (2), 151-166, 1966
Tohoku University Medical Press
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Details 詳細情報について
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- CRID
- 1390282679219072896
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- NII Article ID
- 130003497682
- 10018400217
- 40018682467
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- NII Book ID
- AA00863920
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- COI
- 1:STN:280:DyaF2s%2FgsV2qug%3D%3D
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- ISSN
- 13493329
- 00408727
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- NDL BIB ID
- 8507507
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- PubMed
- 5913197
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- Text Lang
- en
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- Data Source
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- JaLC
- NDL
- Crossref
- PubMed
- CiNii Articles
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- Abstract License Flag
- Disallowed