Brainstem Medulloblastoma Manifesting as Low-tone Sensorineural Hearing Loss

DOI Web Site 15 References

Bibliographic Information

Other Title
  • 一側性感音難聴が初発症状の橋部に発生した髄芽腫例
  • リンショウ イッソクセイ カンオン ナンチョウ ガ ショハツ ショウジョウ ノ キョウブ ニ ハッセイシタ ズイガシュレイ

Search this article

Description

Medulloblastoma is the most common childhood primary central nervous system tumor. In adults, most medulloblastomas occur in patients younger than 40. Common symptoms are cerebellar dysfunction and signs of CSF flow obstruction.<br>This report describes the case of a 25-year-old female who presented with progressive unilateral sensorineural hearing loss (SNHL) as the first symptom of a medulloblastoma in the right inferior cerebellar peduncle and pons. She was referred to an ENT outpatient clinic, and diagnosed with right low tone-dominant SNHL. Her right SNHL progressed with an additional symptom, left moderate facial palsy, 7 months later, and she consequently visited the clinic again. She was introduced to our clinic for further examination. At that time, magnetic resonance imaging (MRI) revealed a right Brainstem lesion. The ipsilateral stapedial reflex was normal in the right ear but absent in the left. Bekesy audiometry was type III. Electronystagmography showed a spontaneous nystagmus to the left and saccade pursuit. The auditory brainstem response was absent in the right ear.<br>The presented case showed that unilateral SNHL can be the first symptom of a brainstem tumor lesion. Progressive SNHL cases should be checked by MRI, in order to exclude brainstem lesions just like cerebello-pontine angle lesions.

Journal

References(15)*help

See more

Keywords

Details 詳細情報について

Report a problem

Back to top