Follicular atrophoderma with multiple basal cell carcinomas. An abortive form of bazex syndrome.

DOI 5 References
  • ARASE Seiji
    Department of Dermatology, Tokushima University School of Medicine
  • NAKANISHI Hideki
    Department of Dermatology, Tokushima University School of Medicine
  • HARADA Shin
    Department of Dermatology, Tokushima University School of Medicine
  • SHIGEMI Fumio
    Department of Dermatology, Tokushima University School of Medicine
  • TAKEDA Katsuyuki
    Department of Dermatology, Tokushima University School of Medicine

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Other Title
  • Ｆｏｌｌｉｃｕｌａｒ　Ａｔｒｏｐｈｏｄｅｒｍａを持つ中年男子にみられた多発性基底細胞癌　　Ｂａｚｅｘ症候群の不完全型か
  • —An Abortive Form of Bazex Syndrome—
  • —Bazex症候群の不完全型か—

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Multiple basal cell carcinomas developed predominantly on the sun exposed areas in a 52-year-old Japanese man. He also had follicular atrophoderma on the extensor aspect of the extremities. Five other siblings were free from symptoms, but his mother suffered from follicular atrophoderma. These findings were consistent with the syndrome described by Bazex et al. However, because the patient lacked other cardinal skin synptoms such as abnormalities of scalp hair and sweating, a diagnosis of an abortive form of Bazex syndrome was made. Numerous basal cell carcinomas were also observed on the trunk, a non-exposed area, previously irradiated with X-rays. We would like to emphasize that radiation therapy should be avoided in patients with Bazex syndrome. Here we report the first case of this rare inherited syndrome in Japan.

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