書誌事項
- タイトル別名
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- A Case of Bullous Amyloidosis
- ショウレイ Bullous Amyloidosis ノ 1レイ
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説明
A 92-year-old man presented with pruritic erythema, blisters and erosions on forearms and dorsum that had persisted for 1-month. Histology of the abdominal erythema showed a subepidermal blister and moderate infiltration of lymphocytes and eosinophils around the dermal blood vessels. Direct immunofluorescence and tests for circulating autoantibodies to pemphigus and pemphigoid were negative. As he had a nephrotic syndrome, a renal biopsy was performed, which disclosed renal and systemic amyloidosis. Direct fast scarlet staining revealed a small amount of amyloid deposit on the bottom of a blister. The amyloids were positive for anti-immunoglobulin λ chain antibody, and were negative for κ chain antibody, transthyretin and AA. A diagnosis of AL amyloidosis was established. He refused a bone marrow puncture, and serum and urine immunoelectrophoresis showed no M-protein and no Bence-Jones protein. Topical corticosteroid and oral antihistamines were not effective in preventing new skin lesions and pruritus. He refused a dialysis and died of renal failure 4 months after the first visit.
収録刊行物
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- 西日本皮膚科
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西日本皮膚科 74 (4), 387-390, 2012
日本皮膚科学会西部支部
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キーワード
詳細情報 詳細情報について
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- CRID
- 1390282679278476288
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- NII論文ID
- 130004475467
- 40019421787
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- NII書誌ID
- AN00183881
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- ISSN
- 18804047
- 03869784
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- NDL書誌ID
- 023959882
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- 本文言語コード
- ja
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- データソース種別
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- JaLC
- NDL
- Crossref
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- 抄録ライセンスフラグ
- 使用不可