Diagnostic criteria for congenital biliary dilatation 2015

  • Hamada Yoshinori
    Kansai Medical University The Japanese Study Group on Pancreaticobiliary Maljunction (JSPBM) The Committee of JSPBM for Diagnostic Criteria for Pancreaticobiliary Maljunction
  • Ando Hisami
    Aichi Prefectural Colony The Japanese Study Group on Pancreaticobiliary Maljunction (JSPBM) The Committee of JSPBM for Diagnostic Criteria for Pancreaticobiliary Maljunction
  • Kamisawa Terumi
    Tokyo Metropolitan Komagome Hospital The Japanese Study Group on Pancreaticobiliary Maljunction (JSPBM) The Committee of JSPBM for Diagnostic Criteria for Pancreaticobiliary Maljunction
  • Itoi Takao
    Tokyo Medical University The Japanese Study Group on Pancreaticobiliary Maljunction (JSPBM) The Committee of JSPBM for Diagnostic Criteria for Pancreaticobiliary Maljunction
  • Urushihara Naoto
    Shizuoka Children's Hospital The Japanese Study Group on Pancreaticobiliary Maljunction (JSPBM) The Committee of JSPBM for Diagnostic Criteria for Pancreaticobiliary Maljunction
  • Koshinaga Tsugumichi
    Nihon University School of Medicine The Japanese Study Group on Pancreaticobiliary Maljunction (JSPBM) The Committee of JSPBM for Diagnostic Criteria for Pancreaticobiliary Maljunction
  • Saito Takeshi
    Chiba University The Japanese Study Group on Pancreaticobiliary Maljunction (JSPBM) The Committee of JSPBM for Diagnostic Criteria for Pancreaticobiliary Maljunction
  • Fujii Hideki
    University of Yamanashi The Japanese Study Group on Pancreaticobiliary Maljunction (JSPBM) The Committee of JSPBM for Diagnostic Criteria for Pancreaticobiliary Maljunction
  • Morotomi Yoshiki
    Osaka City University The Japanese Study Group on Pancreaticobiliary Maljunction (JSPBM) The Committee of JSPBM for Diagnostic Criteria for Pancreaticobiliary Maljunction

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Other Title
  • 先天性胆道拡張症の診断基準2015

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Abstract

Congenital biliary dilatation (CBD) is a congenital malformation involving both extrahepatic bile duct dilatation and pancreaticobiliary maljunction (PBM). Although pathogenesis of bile duct dilatation is unknown, PBM causes reciprocal reflux between the pancreatic juice and bile and results in various biliary and pancreatic pathologies. For a diagnosis of CBD, both abnormal dilatation of the bile duct and PBM must be evident. Bile duct dilatation should be diagnosed based on age-related limits on the maximum diameter of the common bile duct using diagnostic imaging (e.g., ultrasonography, magnetic resonance cholangiopancreatography, and multiplanar reconstruction imaging by multidetector row computed tomography). Endoscopic retrograde cholangiopancreatography, percutaneous transhepatic cholangiopancreatography, and operative cholangiography would be avoided as bile duct measurement tools. Typical concomitant anatomical characteristics of extra- and intra-hepatic bile ducts should be also considered when diagnosing CBD. Diagnosis of PBM, an abnormally long common channel, and/or an abnormal union between the pancreatic and bile ducts must be established by various radiological imaging.

Journal

  • Tando

    Tando 29 (5), 870-873, 2015

    Japan Biliary Association

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