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Agenesis of the corpus callosum and its associated anomalies as pathological background in aicardi syndrome.
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- Tanaka Junichi
- Divisions of Neuropathology Institute of Neurological Sciences, Tottori University School of Medicine
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- Takashima Sachio
- Divisions of Child Neurology Institute of Neurological Sciences, Tottori University School of Medicine
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- Takeshita Kenzo
- Divisions of Child Neurology Institute of Neurological Sciences, Tottori University School of Medicine
Bibliographic Information
- Other Title
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- 脳梁欠損と合併脳奇形 Ａｉｃａｒｄｉ症候群にみられる病理学的背景
- Aicardi症候群にみられる病理学的背景
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Description
Aicardi syndrome is a clinical disease entity consisting of infantile spasms, agenesis of the corpus callosum and chorioretinopathy. Pathologicali dentity of this disorder, however, h as not yet been settled because of extremely rare autopsy cases reported. Agenesis of the corpus callosum generally occurs alone and may coexists with the other malformationss uch as polymicrogyri, aneuronalh eterotopiasa nd lobar hypoplasia. In Aicardi syndrome, the presence of glio-ependymal cysts and choroid plexus papillomas which suggest a hamartomatous growth is characteristic. We reviewed a variety of brain anomalies desecribed in literature and discussedt he pathologicalb ackgroundo f this syndrome
Journal
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- NO TO HATATSU
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NO TO HATATSU 20 (3), 184-190, 1988
THE JAPANESE SOCIETY OF CHILD NEUROLOGY