Congenital Tracheal Stenosis Associated With Biliary Atresia Diagnosed in a Male Infant After Liver Transplantation: A Case Report

Sekine Sachi, Maeda Kosaku, Tazuke Yuko, Yanagisawa Satohiko, Tsuji Yuki

doi:10.11164/jjsps.50.4_814

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胆道閉鎖症術後生体肝移植後に発見された先天性気管狭窄症の1 例
タンドウヘイサショウジュツゴセイタイカンイショクゴニハッケンサレタセンテンセイキカンキョウサクショウノ 1レイ

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Abstract

We report a case with congenital tracheal stenosis associated with biliary atresia in a living-donor liver transplantation. The infantile male patient （age: 1 year 7 months) underwent hepatic porto-enterostomy for biliary atresia at 67-day old. Imperforate anus, hypospadias, and right renal hypoplasia occurred at the same time. He was referred to our hospital transplant surgery when postoperative biliary drainage was not functioning. At the age of 7 months, he was rtificially ventilated due to worsening of the respiratory status attributable to upper respiratory tract infections. Because liver failure has exacerbated, living-part liver transplantation was performed and maintained for 8 months. Because of repeated breathing disorder, he was referred to our department. He was diagnosed with congenital tracheal stenosis. When chronic treatment with an immunosuppressive drug and a steroid was terminated at the age of 1 year 7 months, tracheoplasty was performed. Other than a mild wound infection after surgery, the recovery course was uneventful. Even in an immunosuppressed state after living-donor liver transplantation, a radical surgery of congenital tracheal stenosis was possible in an infantile patient.

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Journal of the Japanese Society of Pediatric Surgeons

Journal of the Japanese Society of Pediatric Surgeons 50 (4), 814-817, 2014

The Japanese Society of Pediatric Surgeons

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