Pulmonary Hypoplasia With Tracheoesophageal Fistula and Duodenal Atresia

  • Ishii Shinji
    Department of Pediatric Surgery, Kurume University School of Medicine
  • Yagi Minoru
    Department of Pediatric Surgery, Kurume University School of Medicine
  • Tanaka Yoshiaki
    Department of Pediatric Surgery, Kurume University School of Medicine
  • Asagiri Kimio
    Department of Pediatric Surgery, Kurume University School of Medicine
  • Asakawa Takahiro
    Department of Pediatric Surgery, Kurume University School of Medicine
  • Tanaka Hiroaki
    Department of Pediatric Surgery, Kurume University School of Medicine
  • Kojima Shinichirou
    Department of Pediatric Surgery, Kurume University School of Medicine
  • Saikusa Nobuyuki
    Department of Pediatric Surgery, Kurume University School of Medicine
  • Hashizume Naoki
    Department of Pediatric Surgery, Kurume University School of Medicine
  • Koga Yoshinori
    Department of Pediatric Surgery, Kurume University School of Medicine

Bibliographic Information

Other Title
  • 著明に拡張した十二指腸と右肺形成不全を伴ったC型食道閉鎖症合併十二指腸閉鎖症の1例
  • 症例報告 著明に拡張した十二指腸と右肺形成不全を伴ったC型食道閉鎖症合併十二指腸閉鎖症の1例
  • ショウレイ ホウコク チョメイ ニ カクチョウ シタ ジュウニシチョウ ト ウハイ ケイセイ フゼン オ トモナッタ Cガタ ショクドウ ヘイサショウ ガッペイ ジュウニシチョウ ヘイサショウ ノ 1レイ

Search this article

Abstract

The patient was born at 37 weeks' gestation after an ultrasound scan at 19 weeks' gestation revealed a possible right-sided abdominal cyst compressing the right diaphragm with hydramnion. MRI at 30 weeks' gestation showed the same findings described above. Passage of a nasogastric tube was unsuccessful after birth. Chest-abdominal x-rays revealed opacification of the right partial hemithorax and large gastric duodenal bubbles with no distal bowel gas. On day 0 of life, duodenoduodenostomy, gastrostomy, and duodenostomy were performed for esophageal atresia and duodenal atresia. In the laparotomy, there was an extremely dilated second portion of the duodenum with distal membranous atresia, and oral side stenosis. On day 24 of age, the esophageal atresia was repaired and hypoplastic lung and elevated right diaphragm were identified. Postoperative bronchofiberscopy showed aplasia of the right middle-lower bronchus. The combined anomalies of pulmonary hypoplasia with esophageal atresia and duodenal atresia are extremely rare. Only 4 cases have been reported in the English literature.

Journal

References(14)*help

See more

Details 詳細情報について

Report a problem

Back to top