A Case of Inflammatory Pseudotumor-like Follicular Dendritic Cell Sarcoma of the Lymph Node in the Small Bowel Mesentery Accompanied by Myasthenia Gravis

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  • KITAGUCHI Daichi
    Department of Gastrointestinal and Hepato-Biliary-Pancreatic Surgery, Faculty of Medicine, University of Tsukuba
  • HISAKURA Katsuji
    Department of Gastrointestinal and Hepato-Biliary-Pancreatic Surgery, Faculty of Medicine, University of Tsukuba
  • SATO Taiki
    Group of Clinical Pathology, University of Tsukuba
  • KURATA Masanao
    Department of Gastrointestinal and Hepato-Biliary-Pancreatic Surgery, Faculty of Medicine, University of Tsukuba
  • ODA Tatsuya
    Department of Gastrointestinal and Hepato-Biliary-Pancreatic Surgery, Faculty of Medicine, University of Tsukuba
  • OHKOHCHI Nobuhiro
    Department of Gastrointestinal and Hepato-Biliary-Pancreatic Surgery, Faculty of Medicine, University of Tsukuba

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Other Title
  • 重症筋無力症合併小腸間膜リンパ節炎症性偽腫瘍型濾胞樹状細胞肉腫の1例
  • 症例 重症筋無力症合併小腸間膜リンパ節炎症性偽腫瘍型濾胞樹状細胞肉腫の1例
  • ショウレイ ジュウショウキン ムリョクショウ ガッペイ ショウチョウ カンマク リンパセツ エンショウセイ ギ シュヨウガタ ロホウジュジョウ サイボウ ニクシュ ノ 1レイ

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A 57-year-old woman presented with ptosis, diplopia, dysarthria, and gait disturbance was diagnosed with myasthenia gravis (MG) and was admitted to our hospital. MRI for lumber spine evaluation revealed a tumor at the mesentery of the small intestine. Tumorectomy and partial resection of the jejunum were performed as the diagnostic treatment. The tumor was composed of proliferation of CD21-positive spindle cells with intense lymphocytic infiltration. Accordingly, it was diagnosed with follicular dendritic cell sarcoma of the inflammatory pseudotumor-like variant (IPT- like FDCS). IPT-like FDCS is an extremely rare tumor, and predominantly affects the liver and the spleen. There have been no reports on IPT-like FDCS which occurred in the lymph node in the mesentery of the small intestine. Furthermore, the relevance of FDCS and MG has been suggested as the paraneoplastic syndrome recently. Our case in which both diseases occurred concomitantly strongly supports the relevance of both diseases. We report the case of IPT-like FDCS occurred in the lymph node in the mesentery of the small intestine accompanied by MG.

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