Successful Catheter Ablation Against Ventricular Tachycardia Associated with Myotonic Dystrophy.

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  • SHIRAISHI Hirokazu
    the Second Department of Medicine, Kyoto Prefectural University of Medicine
  • SHIRAYAMA Takeshi
    the Second Department of Medicine, Kyoto Prefectural University of Medicine
  • INOUE Keiji
    the Second Department of Medicine, Kyoto Prefectural University of Medicine
  • TANAKA Hiroyuki
    the Second Department of Medicine, Kyoto Prefectural University of Medicine
  • KUWABARA Hiroomi
    the Second Department of Medicine, Kyoto Prefectural University of Medicine
  • INOUE Daisuke
    the Second Department of Medicine, Kyoto Prefectural University of Medicine
  • NAKAGAWA Masao
    the Second Department of Medicine, Kyoto Prefectural University of Medicine

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Description

Myotonic dystrophy (MD) is characterized by myotonia and muscular dystrophy and cardiac involvement with tachy-arrhythmia is rarely encountered. We report a case of MD complicated with severe left ventricular hypofunction and incessant ventricular tachycardia (VT) with varying heart rates. The morphology of VT suggested that it originated from the right ventricular outflow tract, and electrophysiological study disclosed that the mechanism of VT was abnormal automaticity. Catheter ablation was performed to treat this VT. The patient had a cardiomyopathy with normal coronary arteries. The specimen of RV biopsy showed moderate hypertrophy, mild fat infiltration and slight fibrosis. These findings are histologically consistent with myotonic dystrophy.<br>(Internal Medicine 39: 39-44, 2000)

Journal

  • Internal Medicine

    Internal Medicine 39 (1), 39-44, 2000

    The Japanese Society of Internal Medicine

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