Retroperitoneal Malignant Peripheral Nerve Sheath Tumor in the Pelvic Cavity without Neurofibromatosis I
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- Obara Shinsaku
- Department of Surgery, Nara Medical University
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- Uchimoto Kazuaki
- Department of Surgery, Nara Medical University
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- Koyama Fumikazu
- Department of Surgery, Nara Medical University Department of Endoscopy and Ultrasound, Nara Medical University
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- Nakagawa Tadashi
- Department of Surgery, Nara Medical University
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- Nakamura Shinji
- Department of Surgery, Nara Medical University
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- Ueda Takeshi
- Department of Surgery, Nara Medical University
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- Nishigori Naoto
- Department of Surgery, Nara Medical University
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- Fujii Hisao
- Department of Endoscopy and Ultrasound, Nara Medical University
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- Tsutsumi Masahiro
- Department of Diagnostic Pathology, Saiseikai Chuwa Hospital
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- Nakajima Yoshiyuki
- Department of Surgery, Nara Medical University
Bibliographic Information
- Other Title
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- 非神経線維腫症の患者にみられた骨盤内悪性末梢神経鞘腫の1例
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Abstract
We present a rare case of malignant peripheral nerve sheath tumor (MPNST) in the pelvic cavity. A 58-year-old woman presented with pain in her buttocks and left leg. She had no signs of neurofibromatosis I. CT and MRI showed a tumor 10 cm in diameter in the pelvic cavity. Since it was very hyperintense on T2-weighted MR imaging, we suspected a neurogenic tumor. Tumor resection, including the capsule, was performed. Histologically, multinuclear tumor cells were seen, and we made a diagnosis of MPNST arising from the pelvic plexus. There are no signs of recurrence 6 years and 3 months after the operation. It is said that about 50% of MPNST are associated with von Recklinghausen neurofibromatosis (NF I). In this case, we could not find any signs of NF I. Furthermore, MPNST are most often located in the limb and the body trunk. We thought that this is a rare case of MPNST originating in the pelvic plexus.
Journal
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- The Japanese Journal of Gastroenterological Surgery
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The Japanese Journal of Gastroenterological Surgery 47 (2), 156-162, 2014
The Japanese Society of Gastroenterological Surgery
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Details 詳細情報について
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- CRID
- 1390282679895263744
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- NII Article ID
- 130004560995
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- ISSN
- 13489372
- 03869768
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- Text Lang
- ja
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- Data Source
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- JaLC
- Crossref
- CiNii Articles
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- Abstract License Flag
- Disallowed