A Case of Klippel-weber Syndrome
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- Iwasaki K.
- Division of Orthopedic Surgery, Ômura National Hospital
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- Inoue Y.
- Division of Orthopedic Surgery, Ômura National Hospital
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- Sasaoka K.
- Division of Dermatology, Ômura National Hospital
Bibliographic Information
- Other Title
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- Klippler-Weber 症候群と思われる1例
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Description
The symptom complex, consisting varicosity, hemangioma and hypertrophy confined to one side of the extremity is generally called “Klippel-Weber Syndrome”<br>The clinical features, however, are full of varieties.<br>An unusual case of Klippel-weber Syndrome in 9-year-old boy is reported. He has had hypertrophies in his right fingers and both lower extremities, hemangioma in trunk and legs, and naevus verrucosus in right side of the body since his birth. The association of hemangioma and naevus verrucosus is corresponded to Adamson-Best type in Phacomatosis Pigmentovascularis (Ota-Kawamura), and very rare in occurence. Angiographic examination in extremities showed venous varicosities, dilatation of veins and probably arteriovenous fistulae. Histologically naevus verrucosus, hemangioma simplex and lymphangioma were seen in right leg. This case, which had hypertrophies of both extremities is thought to be corresponded to “form alterne S. double” by Klippel & Trenaunay.
Journal
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- Orthopedics & Traumatology
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Orthopedics & Traumatology 19 (1), 64-68, 1969
West-Japanese Society of Orthopedics & Traumatology
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Details 詳細情報について
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- CRID
- 1390282679914795776
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- NII Article ID
- 130001637937
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- ISSN
- 13494333
- 00371033
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- Data Source
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- JaLC
- Crossref
- CiNii Articles
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- Abstract License Flag
- Disallowed