Report of a case with severe Wilson-Mikity syndrome cared with home-oxygen therapy

  • Niisato Junko
    Department of Internal Medicine and Rehabilitation Science, Tohoku University Graduate School of Medicine
  • Hoshi Atsushi
    Department of Pediatrics, Iwate Prifectual Hospital
  • Fuchimukai Tohru
    Department of Pediatrics, Iwate Prifectual Hospital
  • Shimada Senji
    Department of Pediatrics, Iwate University School of Medicine
  • Chida Shoichi
    Department of Pediatrics, Iwate University School of Medicine
  • Kurosawa Hajime
    Health Administration Center, Tohoku University
  • Kohzuki Masahiro
    Department of Internal Medicine and Rehabilitation Science, Tohoku University Graduate School of Medicine

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  • 在宅酸素療法を施行した重症Wilson-Mikity syndromeの1例

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<p>在宅酸素療法(home oxygen therapy: HOT)導入後,約3年の経過を観察した重症Wilson-Mikity syndrome (WMS) を報告する.在胎28週6日,体重 1,160 gで出生し,集約的治療が施行された.生後1ヵ月の胸部X線所見,臍帯血 IgM 高値よりWMSと診断した.抜管後も酸素投与を要し,生後約1年1ヵ月で退院,在宅管理へと移行した.現在もHOTを含めた新生児慢性肺疾患の総合的な管理を外来で行っている.今後,成長・発達障害への対策も含めた包括的なリハビリテーションが重要と考えられる.</p>

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