頭蓋内血管周皮腫(SFTの亜型として)の診断、治療と長期予後

書誌事項

タイトル別名
  • Multimodal treatment, long-term outcome, and experience of intracranial meningeal hemangiopericytomas

説明

Intracranial meningeal hemangiopericytoma (M-HPC) is a rare, highly cellular and vascularized mesenchymal tumor that is characterized by high tendency for recurrence and extraneural metastasis.Preoperative images such as CT, MRI, and angiography are necessary for the useful information of M-HPC, although M-HPC shares similar clinical manifestations with meningioma. In distinction from others, radical resection including the attaching dura or dural sinus following adjuvant postoperative radiotherapy remains the cornerstone of therapy in M-HPC. Recently, positive STAT6 immunostaining of the tumor showed that the tumor is different from meningioma, and is the same with the entity of solitary fibrous tumor (SFT). But, advanced molecular study about NAB2-STAT6 fusion gene support the concept that classic SFT and M-HPC are separate groups that share common features but correlate to different clinical outcome.

収録刊行物

詳細情報 詳細情報について

  • CRID
    1390282680481822208
  • NII論文ID
    130005150137
  • DOI
    10.11452/neurooncology.23.1_27
  • ISSN
    21870551
    18800742
  • 本文言語コード
    en
  • データソース種別
    • JaLC
    • CiNii Articles
  • 抄録ライセンスフラグ
    使用不可

問題の指摘

ページトップへ