顎矯正手術を行った筋緊張性ジストロフィーに伴う顎変形症の1例

DOI Web Site Web Site 参考文献4件
  • 池田 順行
    新潟大学大学院医歯学総合研究科顎顔面口腔外科学分野
  • 小原 彰浩
    新潟大学大学院医歯学総合研究科歯科矯正学分野
  • 弦巻 立
    新潟大学大学院医歯学総合研究科歯科麻酔学分野
  • 瀬尾 憲司
    新潟大学大学院医歯学総合研究科歯科麻酔学分野
  • 齋藤 功
    新潟大学大学院医歯学総合研究科歯科矯正学分野
  • 高木 律男
    新潟大学大学院医歯学総合研究科顎顔面口腔外科学分野

書誌事項

タイトル別名
  • A case of jaw deformity with myotonic dystrophy treated by orthognathic surgery
  • ガク キョウセイ シュジュツ オ オコナッタ キン キンチョウセイ ジストロフィー ニ トモナウ ガク ヘンケイショウ ノ 1レイ

この論文をさがす

抄録

<p>Myotonic dystrophy (MyD) is a rare genetic disease characterized by myotonia and muscular atrophy; it is often accompanied by jaw deformity. Orthognathic surgery for MyD has the following disadvantages: various complications can easily occur during general anesthesia, and postoperative mandibular relapse can be caused by masticatory muscle atrophy. We report a case of jaw deformity with MyD treated by orthognathic surgery. A 15-year-old boy visited our department because of abnormal occlusion; mandibular protrusion with anterior open bite was diagnosed. The presence of certain characteristic physical features and the results of genetic examinations led to the diagnosis of MyD. At 18 years of age, he underwent sagittal splitting ramus osteotomy with overcorrection, performed with the patient under general anesthesia in cooperation with related departments. Postoperative intermaxillary fixation was continued for 14 days. The occlusion temporarily stabilized, but a slight anterior open bite appeared 3 months after surgery; therefore, intermaxillary elastic traction was continued for 1.5 years. He has been followed up for 2 years 4 months after surgery, and no relapse has occurred.</p>

収録刊行物

参考文献 (4)*注記

もっと見る

関連プロジェクト

もっと見る

キーワード

詳細情報 詳細情報について

問題の指摘

ページトップへ