Staged Repair of Anomalous Origin of the Right Pulmonary Artery from the Ascending Aorta in a Low Birth Weight Infant : A Surgical Option for the Relief of the Postoperative Right Pulmonary Artery Stenosis

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  • Kawamata Takeshi
    Department of Cardiovascular Surgery, University of Tsukuba Hospital
  • Noma Mio
    Department of Cardiovascular Surgery, University of Tsukuba Hospital
  • Nakajima Tomomi
    Department of Cardiovascular Surgery, University of Tsukuba Hospital
  • Matsubara Muneaki
    Department of Cardiovascular Surgery, University of Tsukuba Hospital
  • Kato Hideyuki
    Department of Cardiovascular Surgery, University of Tsukuba Hospital
  • Tokunaga Chiho
    Department of Cardiovascular Surgery, University of Tsukuba Hospital
  • Sakamoto Hiroaki
    Department of Cardiovascular Surgery, University of Tsukuba Hospital
  • Hiramatsu Yuji
    Department of Cardiovascular Surgery, University of Tsukuba Hospital

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Other Title
  • 心室中隔欠損を伴う右肺動脈上行大動脈起始症の低出生体重児に対する段階的外科修復 —根治術後肺動脈吻合部狭窄の解除に工夫を要した1例—

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<p>A premature boy was born after 35 weeks gestation (1,561 g in weight) with a diagnosis of anomalous origin of the right pulmonary artery from the ascending aorta (AORPA) and perimembranous ventricular septal defect (VSD). The fourteenth day after birth, banding of the right pulmonary artery was performed as a palliative operation. At the age of 5 months (3.9 kg in weight), the right pulmonary artery branched from the ascending aorta, and was anastomosed to a flap made by the lateral wall of the main pulmonary artery with pericardial patch augmentation. VSD patch closure was performed concomitantly. Severe stenosis of the right pulmonary artery compressed by the ascending aorta and left pulmonary hypertension were revealed 3 weeks after the repair. At the age of 11 months, a surgical relief of the right pulmonary artery stenosis was performed. Transection of the ascending aorta provided an excellent exposure of the right posterior pulmonary artery. After patch plasty of the stenotic pulmonary artery, the divided ascending aorta was restored using a strip form patch on 4/5 circle of its posterior wall to extend the aorta and widen the space for the right pulmonary artery. This technique preserves growth potential of the ascending aorta. There are few reports of surgical repair of AORPA with VSD in low birth weight infants. We presented here a case with surgical relief of post-operative right pulmonary artery stenosis. Long term observation of repaired right pulmonary artery, and requiring residual slight hypertension of the left pulmonary artery.</p>

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