A case of branchio-oto-renal syndrome diagnosed with bilateral cervical fistula

DOI
  • FUKUSHIMA Seita
    Department of Otorhinolaryngology, Graduate School of Medical Sciences, Kyushu University Department of Plastic and Reconstructive Surgery, Kyushu University Hospital
  • KAMIZONO Kenichi
    Department of Plastic and Reconstructive Surgery, Kyushu University Hospital
  • KADOTA Hideki
    Department of Plastic and Reconstructive Surgery, Kyushu University Hospital
  • NAKAGAWA Takashi
    Department of Otorhinolaryngology, Graduate School of Medical Sciences, Kyushu University

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Other Title
  • 両側頸瘻を契機に診断された鰓耳腎症候群の 1 例

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Abstract

<p>A 48-year-old man with a history of congenital kidney hypoplasia and hearing loss was referred to our hospital. He had congenital auris fistula and bilateral cervical fistula with a small amount of exudate. The auris fistula had been excised at the department of plastic surgery two months earlier. He had then been admitted to our department for the treatment of the bilateral cervical fistula. The cervical fistula was open at the level of the inferior thyroid cartilage and the anterior margin of the sternocleidomastoid muscle. Computed tomography (CT) was performed after contrast agent was injected via the orifice of fistula. Imaging revealed that the fistula ended outside of the hyoid bone and the tonsillar fossa, with no connection to the pharyngeal space. Three-dimensional CT revealed the structure of the fistula stereoscopically, including its branches. Under general anesthesia, the bilateral cervical fistula was completely removed without injury. The postoperative course was uneventful. It is important to consider branchio-oto-renal syndrome in cases of congenital deafness or branchiogenic malformation, as the early diagnosis can predict complications with kidney disease. Three-dimensional CT was useful for the morphological evaluation and preoperative simulation in the present case.</p>

Journal

  • jibi to rinsho

    jibi to rinsho 63 (6), 211-214, 2017-11-20

    JIBI TO RINSHO KAI

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