Sjögren's Syndrome-associated Pulmonary Amyloidosis Proven by a Transbronchial Cryobiopsy

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  • Ohta Hiroki
    Department of Respiratory Medicine, Saitama Red Cross Hospital
  • Yamakawa Hideaki
    Department of Respiratory Medicine, Saitama Red Cross Hospital Division of Respiratory Diseases, Department of Internal Medicine, Tokyo Jikei University School of Medicine
  • Kato Akari
    Department of Rheumatology, Saitama Red Cross Hospital
  • Horikoshi Masanobu
    Department of Rheumatology, Saitama Red Cross Hospital
  • Sato Shintaro
    Department of Respiratory Medicine, Saitama Red Cross Hospital
  • Akasaka Keiichi
    Department of Respiratory Medicine, Saitama Red Cross Hospital
  • Amano Masako
    Department of Respiratory Medicine, Saitama Red Cross Hospital
  • Matsushima Hidekazu
    Department of Respiratory Medicine, Saitama Red Cross Hospital

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Other Title
  • 経気管支鏡下クライオバイオプシーにより診断したシェーグレン症候群合併肺アミロイドーシスの1例

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<p>Background. Clinicians should consider the possibility of pulmonary amyloidosis as a differential diagnosis of diffuse cystic lung disease. Case. A 72-year-old man was referred to our hospital because of a chest abnormality with multiple pulmonary cysts under a diagnosis of polymyalgia rheumatica and Sjögren's syndrome. A transbronchial lung cryobiopsy revealed amyloid deposition in the bronchus, pulmonary artery wall, and alveolar septum, so we diagnosed him with pulmonary amyloidosis associated with Sjögren's syndrome. In addition, we speculated that the pulmonary cysts had been caused by the loss of elastic fibers in the alveolar walls due to amyloid deposition. Conclusion. A transbronchial lung cryobiopsy is considered a useful strategy for the diagnosis and elucidation of various conditions in pulmonary amyloidosis.</p>

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