口蓋裂を伴うまれな巨大咽頭奇形腫切除後口蓋欠損に対して二段階口蓋閉鎖術を行った 1 例

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  • Reconstruction of a Large Palatal Defect by Two-Stage Palatoplasty after Excision of a Rare Giant Neonatal Pharyngeal Teratoma: A Case Report

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<p>　　Neonatal oropharyngeal teratoma (=epignathus) is a markedly rare congenital malformation, with an incidence of 1 in 35,000-200,000 live births. Regarding deformities associated with this tumor, cleft palate is common. We report a rare case of epignathus in a male newborn with a huge oral mass protruding through a cleft in the hard palate.<BR>　　For the large defect of the palate after surgical excision of the tumor, soft and hard palate closure were performed at 2 years and 11 months, and 5 years and 4 months, respectively. As a result, language development is age-appropriate and velopharyngeal insufficiency is mild, but the patient was able to produce monophonic words approximately 4 years after the second surgery. There is no malocclusion or rhinorrhea on ingestion at 9 years of age.<BR>　　The two-stage operation resulted in insufficient velopharyngeal closure function in many reports; however, language training resulted in good language performance equivalent to that after the one-stage operation.<BR>　　This report describes our procedure and postoperative course.</p>

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