A Case of Mesenteric Desmoid-type Fibromatosis

DOI
  • Ogawa Nami
    Department of ultrasonographic examination, Kameda Medical Center Hospital
  • Kitaura Koichi
    Department of ultrasonographic examination, Kameda Medical Center Hospital
  • Komiya Masaaki
    Department of ultrasonographic examination, Kameda Medical Center Hospital
  • Kohara Masami
    Department of ultrasonographic examination, Kameda Medical Center Hospital
  • Yamamura Kazuhiro
    Department of ultrasonographic examination, Kameda Medical Center Hospital
  • Sasaki Miwa
    Department of ultrasonographic examination, Kameda Medical Center Hospital
  • Kanawa Tomoko
    Department of ultrasonographic examination, Kameda Medical Center Hospital
  • Homma Yoshiyuki
    Department of ultrasonographic examination, Kameda Medical Center Hospital
  • Kansaku Shinya
    Department of ultrasonographic examination, Kameda Medical Center Hospital
  • Hasegawa Takashi
    Department of ultrasonographic examination, Kameda Medical Center Hospital
  • Arai Yuta
    Department of ultrasonographic examination, Kameda Medical Center Hospital
  • Saito Hiroya
    Department of ultrasonographic examination, Kameda Medical Center Hospital
  • Hirata Nobuto
    Department of Gastroenterology, Kameda Medical Center Hospital
  • Sato Takahisa
    Department of Gastroenterology, Teikyo University Chiba Medical Center

Bibliographic Information

Other Title
  • 腸間膜デスモイド型線維腫症の1例

Abstract

<p>腸間膜デスモイド型線維腫症は，緩徐に成長するまれな線維腫症の一種である．腸間膜腫瘍は，特徴的な画像所見がないことから術前診断は困難なことが多い．今回我々は，まれな疾患である腸間膜デスモイド型線維腫症の1例を経験したので報告する．症例は60代，男性．他院の人間ドックで腹腔内腫瘍を指摘され，当院消化器内科紹介受診．腹部超音波検査で右腹部に59×50 mmの類球形低エコー腫瘤像を認めた．輪郭整，内部不均一で一部に血流シグナルを認めた．体位変換で可動性を認め，小腸もしくは腸間膜由来と考えた．腫瘤は小腸筋層と連続している印象があり，小腸由来の消化管間質腫瘍を第一に考え，鑑別に線維腫，線維肉腫など腸間膜由来の腫瘍を考えた．精査の結果，小腸由来の消化管間質腫瘍疑いで手術となった．病理組織検査では核分裂像を認めない線維芽細胞と膠原線維の増殖像を認め，腫瘍は小腸筋層に浸潤していた．免疫染色ではCD34, c-kit, S100, SMAがいずれも陰性，β-catenin陽性で，デスモイド型線維腫症と診断された．</p>

Journal

Keywords

Details 詳細情報について

  • CRID
    1390581157740354560
  • DOI
    10.11272/jss.410
  • ISSN
    18814514
    18814506
  • Text Lang
    ja
  • Data Source
    • JaLC
  • Abstract License Flag
    Disallowed

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