A case of neuroendocrine tumor (NET) of the ampulla of Vater and gastrointestinal stromal tumor (GIST) of duodenum with neurofibromatosis type 1 (NF1)
-
- Kozuki Akihito
- Department of Surgery, Kakogawa Central City Hospital
-
- Sawa Hidehiro
- Department of Surgery, Kakogawa Central City Hospital
-
- Hirata Yuichi
- Department of Gastroenterology, Kakogawa Central City Hospital
-
- Okabe Yoshihiro
- Department of Gastroenterology, Kakogawa Central City Hospital
-
- Kitamura Satoru
- Department of Diagnostic Pathology, Kakogawa Central City Hospital
-
- Imai Yukihiro
- Department of Diagnostic Pathology, Kakogawa Central City Hospital
Bibliographic Information
- Other Title
-
- 神経線維腫症1型に合併した十二指腸乳頭部神経内分泌腫瘍および十二指腸gastrointestinal stromal tumorの1例
Search this article
Description
<p>We describe the case of a 71-year-old woman with neurofibromatosis type-1 (NF1) diagnosed with a neuroendocrine tumor (NET) of the ampulla of Vater and a gastrointestinal stromal tumor (GIST) of the duodenum. The patient was admitted to our hospital and presented with multiple cutaneous neurofibromas and café-au-lait spots on the face and body. Esophagogastroduodenoscopy revealed an exposed protruding tumor of the Vater and a submucosal tumor in the descending part of the duodenum. CT showed both tumors, but somatostatin receptor scintigraphy visualized no tumor in the duodenum. The patient was diagnosed with NET of the Vater and GIST of the duodenum based on histopathological examination of biopsy specimens, and subsequently underwent subtotal stomach-preserving pancreaticoduodenectomy with regional lymph node dissection. Histopathological examination after the procedure confirmed NET (G1) of the Vater with lymph node metastases and GIST of the duodenum.</p>
Journal
-
- Tando
-
Tando 33 (4), 734-743, 2019-10-31
Japan Biliary Association
- Tweet
Details 詳細情報について
-
- CRID
- 1390845702309784192
-
- NII Article ID
- 130007738980
-
- ISSN
- 18836879
- 09140077
-
- Text Lang
- ja
-
- Data Source
-
- JaLC
- CiNii Articles
-
- Abstract License Flag
- Disallowed