A Case of Jejunal Mucosal Patch Repair for Local Excision of a Duodenal Gastrointestinal Stromal Tumor Associated with Neurofibromatosis Type 1

HIGASHI Yuri, YAMASAKI Yuki, TSUKADA Tomoya, AOKI Tatsuya, KAJI Masahide, SHIMIZU Koichi

doi:10.3919/jjsa.80.2018

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Other Title

切除後に有茎空腸粘膜パッチ再建した神経線維腫症1型合併十二指腸GISTの1例
症例切除後に有茎空腸粘膜パッチ再建した神経線維腫症1型合併十二指腸GISTの1例
ショウレイセツジョゴニユウケイクウチョウネンマクパッチサイケンシタシンケイセンイシュショウ 1ガタガッペイジュウニシチョウ GIST ノ 1レイ

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Abstract

<p>Two years ago, a 57-year-old woman with neurofibromatosis type 1 (NF1) underwent an abdominal hysterectomy for a uterine myoma and a wedge-shaped excision of the jejunum for gastrointestinal stromal tumor (GIST). A follow-up computed tomography revealed a 32-mm tumor in the duodenum, and endoscopic findings revealed a submucosal tumor on the contralateral and anal side of the duodenal papilla. Hence, a diagnosis of duodenal GIST was made and an open surgery was performed. A part of the jejunum (15 cm in length) was removed using local excision and a jejunal mucosal patch was grafted. After the surgery, no deformation or stenosis of the surgical lesion was found following fluoroscopy. In general, 7% of NF1 patients have GISTs, and 68% of the lesions often occur in multiples in the small intestine. The malignancies are often low grade. There is an increased risk in surgery and reconstruction when a large lesion is located in the duodenum ; however, it is possible to prevent deformation and stenosis using a jejunal mucosal patch for the duodenal defect.</p>

Journal

Nihon Rinsho Geka Gakkai Zasshi (Journal of Japan Surgical Association)

Nihon Rinsho Geka Gakkai Zasshi (Journal of Japan Surgical Association) 80 (11), 2018-2022, 2019

Japan Surgical Association

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