Beckwith-Wiedemann syndrome with infantile hepatic hemangiomas

DOI
  • Adachi Natsuho
    Department of Pediatrics, The University of Tokyo Hospital Department of Pediatrics, Chigasaki Municipal Hospital
  • Irisa Chiharu
    Department of Pediatrics, The University of Tokyo Hospital
  • Kashima Kohei
    Department of Pediatrics, The University of Tokyo Hospital
  • Kakiuchi Satsuki
    Department of Pediatrics, The University of Tokyo Hospital
  • Nishimura Riki
    Department of Pediatrics, The University of Tokyo Hospital
  • Takami Shohei
    Department of Pediatric Surgery, The University of Tokyo Hospital
  • Watanabe Miho
    Osaka University Graduate School of Medicine, Department of Pediatric Surgery
  • Takahashi Naoto
    Department of Pediatrics, The University of Tokyo Hospital

Bibliographic Information

Other Title
  • Beckwith-Wiedemann症候群の超早産児で多発乳児肝血管腫を合併した1例

Search this article

Abstract

<p> A 2-month-old female with Beckwith-Wiedemann syndrome, delivered at a gestational age of 25 weeks and birth weight 1, 083g, developed multiple liver masses. It was difficult to differentiate hepatoblastoma from hepatic hemangioma because she was too immature to perform a liver biopsy. We used, therefore, propranolol hydrochloride as a therapeutic and diagnostic treatment although it is not recommended to use for preterm infants in general. The patient showed a decrease tumor size significantly, which led to diagnosis as infantile hepatic hemangiomas.</p><p> We suggest that propranolol hydrochloride may be useful to manage preterm infants with liver tumors suspected as infantile hepatic hemangioma.</p>

Journal

Related Projects

See more

Keywords

Details 詳細情報について

Report a problem

Back to top