A Case of Infantile Myofibromatosis (Solitary Type) With Small Bowel Stenosis

Fumita Takashi, Nakata Mitsuyuki, Terui Keita, Komatsu Shugo, Ohno Sachie, Mise Naoko, Oita Satoru, Saito Takeshi, Ota Masayuki, Hishiki Tomoro

doi:10.11164/jjsps.58.5_799

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小腸狭窄をきたした乳幼児筋線維腫症（infantile myofibromatosis, solitary type）の1例
ショウチョウキョウサクオキタシタニュウヨウジキンセンイシュショウ(infantile myofibromatosis, solitary type)ノ 1レイ

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Abstract

<p>The patient was an 11-day-old female who presented with bilious vomiting. Low-allergen formula was given for the putative diagnosis of milk allergy, but the bilious vomiting persisted. She was transferred to our hospital and an upper gastrointestinal contrast study demonstrated a jejunal stenosis 50 cm on the anal side from the ligament of Treitz. She was diagnosed as having congenital jejunal stenosis and laparotomy was performed. A stenotic lesion was found in the jejunum at 45 cm from the ligament of Treitz. The lesion was resected, and the jejunum was repaired by an end-to-end anastomosis. The lumen of the specimen was occupied by a mass, that caused intestinal obstruction. The patient was started on oral feeding on postoperative day 4 and was discharged on postoperative day 25 after an uneventful course. Microscopic examination of the resected mass revealed a bundle-like proliferation of spindle-shaped cells with ellipse nuclei, and the histopathological diagnosis was infantile myofibromatosis (solitary type). Systemic exploration demonstrated no mass lesions elsewhere, and no postoperative treatment was given. She remains healthy without recurrence after six years.</p>

Journal

Journal of the Japanese Society of Pediatric Surgeons

Journal of the Japanese Society of Pediatric Surgeons 58 (5), 799-803, 2022-08-20

The Japanese Society of Pediatric Surgeons

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