A Case of Failing Fontan with Pulmonary Vein Occlusion Obtained Decrease in the Central Venous Pressure by Fenestration Creation after Embolization of Minor Aortopulmonary Collateral Artery and Pulmonary Artery
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- Baba Shigehito
- Department of Pediatrics, Niigata University Graduate School of Medical and Dental Sciences
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- Abe Tadaaki
- Department of Pediatrics, Niigata University Graduate School of Medical and Dental Sciences
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- Tsukada Masanori
- Department of Pediatrics, Niigata University Graduate School of Medical and Dental Sciences
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- Ozawa Junichi
- Department of Pediatrics, Niigata University Graduate School of Medical and Dental Sciences
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- Sugimoto Ai
- Department of Thoracic and Cardiovascular Surgery, Niigata University Graduate School of Medical and Dental Sciences
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- Numano Fujito
- Department of Pediatrics, Niigata University Graduate School of Medical and Dental Sciences
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- Shiraishi Shuichi
- Department of Thoracic and Cardiovascular Surgery, Niigata University Graduate School of Medical and Dental Sciences
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- Saito Akihiko
- Department of Pediatrics, Niigata University Graduate School of Medical and Dental Sciences
Bibliographic Information
- Other Title
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- 体肺側副血管と肺動脈の塞栓後に開窓作成術を行い中心静脈圧の低下が得られた肺静脈閉塞を合併したFailing Fontanの一例
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Description
<p>No effective treatments currently exist for patients who have undergone the Fontan procedure with pulmonary vein occlusion (PVO), and the prognosis is poor. We present a case of a 3-year-old girl with acute heart failure who developed right PVO after undergoing the Fontan procedure, and a large amount of pleural effusion, edema, and atrial arrhythmia was noted. Fenestration was created after embolization of the minor aortopulmonary collateral arteries (mAPCAs) and right pulmonary (RPA) artery. The embolization of mAPCAs was divided into 3 sessions using 51 coils. For RPA embolization, 5 Amplatzer Vascular Plugs and 2 coils were used. The duration of this procedure was approximately 3 h, and complete occlusion of RPA was achieved without complications. Subsequently, fenestration creation was performed, and the central venous pressure decreased from 20 mmHg to 7 mmHg. However, the patient deceased because of cardiac tamponade on day 9 postoperatively. To our knowledge, there have been no reports on the complete embolization of the mAPCAs and PA in patients who have undergone the Fontan procedure with PVO. This treatment temporarily stabilized the hemodynamics in patients who have undergone the Fontan procedure with PVO.</p>
Journal
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- Pediatric Cardiology and Cardiac Surgery
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Pediatric Cardiology and Cardiac Surgery 37 (4), 320-328, 2021-12-01
Japanese Society of Pediatric Cardiology and Cardiac Surgery
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Keywords
Details 詳細情報について
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- CRID
- 1390856207410833664
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- ISSN
- 21872988
- 09111794
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- Text Lang
- ja
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- Data Source
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- JaLC
- Crossref
- KAKEN
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- Abstract License Flag
- Disallowed