A Case of Solitalry Gastric Gastrointestinal Stromal Tumor Associated with Neurofibromatosis Type 1 Locally Resected by Laparoscopic and Endoscopic Cooperative Surgery

YAMADA Jun, KITAMURA Chieko, KATO Daiki

doi:10.3919/jjsa.84.1604

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Other Title

腹腔鏡内視鏡合同胃局所切除術を行った神経線維腫症1型関連胃GISTの1例
フククウキョウナイシキョウゴウドウイキョクショセツジョジュツオオコナッタシンケイセンイシュショウ 1ガタカンレンイ GIST ノ 1レイ

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Abstract

<p>A 40-year-old male patient with neurofibromatosis type 1 (NF1) underwent upper gastrointestinal series for epigastric discomfort and was diagnosed as having a 30-mm sized, gastrointestinal stromal tumor (GIST) with intraluminal growth pattern at the upper body of the stomach. A thoracoabdominal CT scan demonstrated no other lesions in our case, however, NF1-related GISTs often occur in the small intestine and prone to develop in multiple organs. Accordingly, it would be important for operative procedure not only to resect gastric GIST but also to confirm the absence of other lesions in the abdominal cavity. At surgery, we confirmed the absence of other lesions by close laparoscopic observation of the abdominal cavity, and then performed local gastric resection for gastric GIST by means of laparoscopic and endoscopic cooperative surgery (LECS). The postoperative course was uneventful and no recurrence has occurred as of 4 years after the operation.</p><p>It is very rare that NF1-related GIST occurs solitary in the stomach. If GIST of the stomach is detected in a NF1 patient, we must keep a possibility of the presence of other lesions in mind ; and even in a case in which preoperative imaging did not show any other lesions, we should actively perform intraoperative survey. As the procedure, laparoscopic observation may be useful in terms of minimal invasiveness.</p>

Journal

Nihon Rinsho Geka Gakkai Zasshi (Journal of Japan Surgical Association)

Nihon Rinsho Geka Gakkai Zasshi (Journal of Japan Surgical Association) 84 (10), 1604-1610, 2023

Japan Surgical Association

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