A Case of T Cell Lymphoma Initially Diagnosed as Lipogranulomatosis Subcutanea(Rothmann-Makai Syndrome).

DOI 16 References

Bibliographic Information

Other Title
  • 皮下脂肪肉芽腫症（Ｒｏｔｈｍａｎｎ‐Ｍａｋａｉ症侯群）様皮疹にて発症したＴ　Ｃｅｌｌ　Ｌｙｍｐｈｏｍａ

Description

A 57-year-old woman presented with multiple subcutaneous nodules was diagnosed at first as lipogranulomatosis subcutanea (Rothmann-Makai syndrome), since the nodules showed histologically lipogranulomas and infiltration of neutrophils, lymphocytes, giant cells and foam cells, while the patient also had no systemic symptoms. Although the nodules spontaneously subsided after the diagnosis, six months later she developed multiple, large and deep skin ulcers associated with exudative erythemas. A biopsy specimen of the exudative erythema showed medium-sized atypical lymphoid cells in the dermis and the subcutaneous tissue. The diagnosis of T cell lymphoma was made since the cells were positive for MT1 and UCHL-1 staining, but negative for L26 staining. Biopsies specimens of the other tissue revealed the involvement of the nasal mucous tissue and right inguinal lymph nodes. A cytologic examination of the aqueous humor showed Pap. class III. Diagnostic imaging indicated the involvement of lymphoma cells in the pancreas and the kidney. She was treated by chemotherapy, but eventually died one and a half years after the first diagnosis.

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Details 詳細情報について

  • CRID
    1390001204299969152
  • NII Article ID
    130004831001
  • DOI
    10.2336/nishinihonhifu.56.984
  • ISSN
    18804047
    03869784
  • Text Lang
    ja
  • Data Source
    • JaLC
    • Crossref
    • CiNii Articles
  • Abstract License Flag
    Disallowed

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